TermID Term Enrichment logP Genes in Term Target Genes in Term Fraction of Targets in Term Total Target Genes Total Genes Entrez Gene IDs Gene Symbols SMP02298 Glutaminolysis and Cancer 4.53058954219039e-05 -10.0020733921791 35 16 0.0958083832335329 167 992 6390,6509,8802,2806,3419,4191,47,3939,1431,6566,8801,2746,4967,3420,6389,51660 SDHB,SLC1A4,SUCLG1,GOT2,IDH3A,MDH2,ACLY,LDHA,CS,SLC16A1,SUCLG2,GLUD1,OGDH,IDH3B,SDHA,MPC1 SMP00390 Tay-Sachs Disease 9.43618165904271e-05 -9.26837405190995 17 10 0.0598802395209581 167 992 55907,6675,64841,10007,10020,54187,51005,26503,140838,3073 CMAS,UAP1,GNPNAT1,GNPDA1,GNE,NANS,AMDHD2,SLC17A5,NANP,HEXA SMP00045 Amino Sugar Metabolism 9.43618165904271e-05 -9.26837405190995 17 10 0.0598802395209581 167 992 55907,6675,64841,10007,10020,54187,51005,26503,140838,3073 CMAS,UAP1,GNPNAT1,GNPDA1,GNE,NANS,AMDHD2,SLC17A5,NANP,HEXA SMP00240 Salla Disease/Infantile Sialic Acid Storage Disease 9.43618165904271e-05 -9.26837405190995 17 10 0.0598802395209581 167 992 55907,6675,64841,10007,10020,54187,51005,26503,140838,3073 CMAS,UAP1,GNPNAT1,GNPDA1,GNE,NANS,AMDHD2,SLC17A5,NANP,HEXA SMP00534 G(M2)-Gangliosidosis: Variant B- Tay-sachs disease 9.43618165904271e-05 -9.26837405190995 17 10 0.0598802395209581 167 992 55907,6675,64841,10007,10020,54187,51005,26503,140838,3073 CMAS,UAP1,GNPNAT1,GNPDA1,GNE,NANS,AMDHD2,SLC17A5,NANP,HEXA SMP00216 Sialuria or French Type Sialuria 9.43618165904271e-05 -9.26837405190995 17 10 0.0598802395209581 167 992 55907,6675,64841,10007,10020,54187,51005,26503,140838,3073 CMAS,UAP1,GNPNAT1,GNPDA1,GNE,NANS,AMDHD2,SLC17A5,NANP,HEXA SMP00217 Sialuria or French Type Sialuria 9.43618165904271e-05 -9.26837405190995 17 10 0.0598802395209581 167 992 55907,6675,64841,10007,10020,54187,51005,26503,140838,3073 CMAS,UAP1,GNPNAT1,GNPDA1,GNE,NANS,AMDHD2,SLC17A5,NANP,HEXA SMP00548 Mitochondrial complex II deficiency 0.000561100406804178 -7.48561069019571 20 10 0.0598802395209581 167 992 6390,8802,3419,4191,1431,8801,4967,3420,6389,51660 SDHB,SUCLG1,IDH3A,MDH2,CS,SUCLG2,OGDH,IDH3B,SDHA,MPC1 SMP00057 Citric Acid Cycle 0.000561100406804178 -7.48561069019571 20 10 0.0598802395209581 167 992 6390,8802,3419,4191,1431,8801,4967,3420,6389,51660 SDHB,SUCLG1,IDH3A,MDH2,CS,SUCLG2,OGDH,IDH3B,SDHA,MPC1 SMP00551 Pyruvate dehydrogenase deficiency (E2) 0.000561100406804178 -7.48561069019571 20 10 0.0598802395209581 167 992 6390,8802,3419,4191,1431,8801,4967,3420,6389,51660 SDHB,SUCLG1,IDH3A,MDH2,CS,SUCLG2,OGDH,IDH3B,SDHA,MPC1 SMP00546 Congenital lactic acidosis 0.000561100406804178 -7.48561069019571 20 10 0.0598802395209581 167 992 6390,8802,3419,4191,1431,8801,4967,3420,6389,51660 SDHB,SUCLG1,IDH3A,MDH2,CS,SUCLG2,OGDH,IDH3B,SDHA,MPC1 SMP00549 2-ketoglutarate dehydrogenase complex deficiency 0.000561100406804178 -7.48561069019571 20 10 0.0598802395209581 167 992 6390,8802,3419,4191,1431,8801,4967,3420,6389,51660 SDHB,SUCLG1,IDH3A,MDH2,CS,SUCLG2,OGDH,IDH3B,SDHA,MPC1 SMP00547 Fumarase deficiency 0.000561100406804178 -7.48561069019571 20 10 0.0598802395209581 167 992 6390,8802,3419,4191,1431,8801,4967,3420,6389,51660 SDHB,SUCLG1,IDH3A,MDH2,CS,SUCLG2,OGDH,IDH3B,SDHA,MPC1 SMP00550 Pyruvate dehydrogenase deficiency (E3) 0.000561100406804178 -7.48561069019571 20 10 0.0598802395209581 167 992 6390,8802,3419,4191,1431,8801,4967,3420,6389,51660 SDHB,SUCLG1,IDH3A,MDH2,CS,SUCLG2,OGDH,IDH3B,SDHA,MPC1 SMP00445 Spermidine and Spermine Biosynthesis 0.000665947343619136 -7.31429995418451 6 5 0.029940119760479 167 992 27430,6723,4953,4144,262 MAT2B,SRM,ODC1,MAT2A,AMD1 SMP02358 The oncogenic action of L-2-hydroxyglutarate in Hydroxygluaricaciduria 0.000904019015834053 -7.00866016257867 28 12 0.0718562874251497 167 992 6390,22992,8802,3419,4191,1431,8801,2746,4967,3420,6389,51660 SDHB,KDM2A,SUCLG1,IDH3A,MDH2,CS,SUCLG2,GLUD1,OGDH,IDH3B,SDHA,MPC1 SMP00654 Warburg Effect 0.00112003253312136 -6.79439754666722 44 16 0.0958083832335329 167 992 8802,3419,7086,2746,4967,5315,6389,51660,6390,1431,8801,6566,4190,2821,6888,3420 SUCLG1,IDH3A,TKT,GLUD1,OGDH,PKM,SDHA,MPC1,SDHB,CS,SUCLG2,SLC16A1,MDH1,GPI,TALDO1,IDH3B SMP02359 The oncogenic action of D-2-hydroxyglutarate in Hydroxygluaricaciduria 0.00131808753384048 -6.63157343096414 29 12 0.0718562874251497 167 992 6390,22992,8802,3419,4191,1431,8801,2746,4967,3420,6389,51660 SDHB,KDM2A,SUCLG1,IDH3A,MDH2,CS,SUCLG2,GLUD1,OGDH,IDH3B,SDHA,MPC1 SMP02291 The oncogenic action of 2-hydroxyglutarate 0.00170257552812613 -6.37561315785494 26 11 0.0658682634730539 167 992 6390,22992,8802,3419,4191,1431,8801,4967,3420,6389,51660 SDHB,KDM2A,SUCLG1,IDH3A,MDH2,CS,SUCLG2,OGDH,IDH3B,SDHA,MPC1 SMP02292 The oncogenic action of Succinate 0.00187782293905391 -6.27764218429479 30 12 0.0718562874251497 167 992 6390,22992,8802,3419,4191,1431,8801,4967,3420,6389,51660,54583 SDHB,KDM2A,SUCLG1,IDH3A,MDH2,CS,SUCLG2,OGDH,IDH3B,SDHA,MPC1,EGLN1 SMP02295 The oncogenic action of Fumarate 0.00187782293905391 -6.27764218429479 30 12 0.0718562874251497 167 992 6390,22992,8802,3419,4191,1431,8801,4967,3420,6389,51660,54583 SDHB,KDM2A,SUCLG1,IDH3A,MDH2,CS,SUCLG2,OGDH,IDH3B,SDHA,MPC1,EGLN1 SMP00603 Gemcitabine Metabolism Pathway 0.0127218678037591 -4.36443289193192 13 6 0.0359281437125748 167 992 6241,1635,2030,1633,1503,6240 RRM2,DCTD,SLC29A1,DCK,CTPS1,RRM1 SMP00446 Gemcitabine Action Pathway 0.0127218678037591 -4.36443289193192 13 6 0.0359281437125748 167 992 6241,1635,2030,1633,1503,6240 RRM2,DCTD,SLC29A1,DCK,CTPS1,RRM1 SMP00129 Malate-Aspartate Shuttle 0.0164615063518694 -4.1067305720111 4 3 0.0179640718562874 167 992 8604,2806,4191 SLC25A12,GOT2,MDH2 SMP00320 Intracellular Signalling Through Adenosine Receptor A2a and Adenosine 0.0168305072105025 -4.08456213394878 38 12 0.0718562874251497 167 992 2778,4216,5170,5906,998,6195,1385,2002,5594,1386,3265,5605 GNAS,MAP3K4,PDPK1,RAP1A,CDC42,RPS6KA1,CREB1,ELK1,MAPK1,ATF2,HRAS,MAP2K2 SMP00321 Intracellular Signalling Through Adenosine Receptor A2b and Adenosine 0.0168305072105025 -4.08456213394878 38 12 0.0718562874251497 167 992 2778,4216,5170,5906,998,6195,1385,2002,5594,1386,3265,5605 GNAS,MAP3K4,PDPK1,RAP1A,CDC42,RPS6KA1,CREB1,ELK1,MAPK1,ATF2,HRAS,MAP2K2 SMP00391 Insulin Signalling 0.0248064112447225 -3.69665314128885 11 5 0.029940119760479 167 992 5170,5594,3265,5605,5894 PDPK1,MAPK1,HRAS,MAP2K2,RAF1 SMP00340 Methylenetetrahydrofolate Reductase Deficiency (MTHFRD) 0.0282108846995483 -3.56804739325657 19 7 0.0419161676646707 167 992 27430,6723,191,4548,1786,4144,262 MAT2B,SRM,AHCY,MTR,DNMT1,MAT2A,AMD1 SMP00214 S-Adenosylhomocysteine (SAH) Hydrolase Deficiency 0.0282108846995483 -3.56804739325657 19 7 0.0419161676646707 167 992 27430,6723,191,4548,1786,262,4144 MAT2B,SRM,AHCY,MTR,DNMT1,AMD1,MAT2A SMP00221 Methionine Adenosyltransferase Deficiency 0.0282108846995483 -3.56804739325657 19 7 0.0419161676646707 167 992 27430,6723,191,4548,1786,4144,262 MAT2B,SRM,AHCY,MTR,DNMT1,MAT2A,AMD1 SMP00177 Cystathionine Beta-Synthase Deficiency 0.0282108846995483 -3.56804739325657 19 7 0.0419161676646707 167 992 27430,6723,191,4548,1786,4144,262 MAT2B,SRM,AHCY,MTR,DNMT1,MAT2A,AMD1 SMP00341 Hypermethioninemia 0.0282108846995483 -3.56804739325657 19 7 0.0419161676646707 167 992 27430,6723,191,4548,1786,262,4144 MAT2B,SRM,AHCY,MTR,DNMT1,AMD1,MAT2A SMP00033 Methionine Metabolism 0.0282108846995483 -3.56804739325657 19 7 0.0419161676646707 167 992 27430,6723,191,4548,1786,4144,262 MAT2B,SRM,AHCY,MTR,DNMT1,MAT2A,AMD1 SMP00222 Glycine N-methyltransferase Deficiency 0.0282108846995483 -3.56804739325657 19 7 0.0419161676646707 167 992 27430,6723,191,4548,1786,4144,262 MAT2B,SRM,AHCY,MTR,DNMT1,MAT2A,AMD1 SMP00570 Homocystinuria-megaloblastic anemia due to defect in cobalamin metabolism- cblG complementation type 0.0282108846995483 -3.56804739325657 19 7 0.0419161676646707 167 992 27430,6723,191,4548,1786,4144,262 MAT2B,SRM,AHCY,MTR,DNMT1,MAT2A,AMD1 SMP00466 Transfer of Acetyl Groups into Mitochondria 0.0311307801876376 -3.46955823259926 8 4 0.0239520958083832 167 992 4190,51660,47,1431 MDH1,MPC1,ACLY,CS SMP00123 Betaine Metabolism 0.0311307801876376 -3.46955823259926 8 4 0.0239520958083832 167 992 27430,191,4548,4144 MAT2B,AHCY,MTR,MAT2A SMP00428 Mercaptopurine Action Pathway 0.0391292270541172 -3.24088559623585 47 13 0.0778443113772455 167 992 159,2618,7295,2987,471,2983,5879,6240,3614,158,6241,2030,10057 ADSS,GART,TXN,GUK1,ATIC,GUCY1B1,RAC1,RRM1,IMPDH1,ADSL,RRM2,SLC29A1,ABCC5 SMP00430 Thioguanine Action Pathway 0.0391292270541172 -3.24088559623585 47 13 0.0778443113772455 167 992 159,2618,7295,2987,2983,471,5879,6240,3614,158,6241,2030,10057 ADSS,GART,TXN,GUK1,GUCY1B1,ATIC,RAC1,RRM1,IMPDH1,ADSL,RRM2,SLC29A1,ABCC5 SMP00427 Azathioprine Action Pathway 0.0391292270541172 -3.24088559623585 47 13 0.0778443113772455 167 992 159,2618,7295,2987,2983,471,5879,6240,3614,158,6241,2030,10057 ADSS,GART,TXN,GUK1,GUCY1B1,ATIC,RAC1,RRM1,IMPDH1,ADSL,RRM2,SLC29A1,ABCC5 SMP00580 GLUT-1 deficiency syndrome 0.0488130166738042 -3.01975826657158 9 4 0.0239520958083832 167 992 124583,2683,7360,6513 CANT1,B4GALT1,UGP2,SLC2A1 SMP00444 Lactose Synthesis 0.0488130166738042 -3.01975826657158 9 4 0.0239520958083832 167 992 124583,2683,7360,6513 CANT1,B4GALT1,UGP2,SLC2A1 SMP00579 Congenital disorder of glycosylation CDG-IId 0.0488130166738042 -3.01975826657158 9 4 0.0239520958083832 167 992 2683,124583,7360,6513 B4GALT1,CANT1,UGP2,SLC2A1 SMP00464 Vitamin K Metabolism 0.075198289986083 -2.58762678783166 3 2 0.0119760479041916 167 992 79001,1728 VKORC1,NQO1 SMP00459 Pyruvaldehyde Degradation 0.075198289986083 -2.58762678783166 3 2 0.0119760479041916 167 992 2739,3029 GLO1,HAGH SMP00203 Molybdenum Cofactor Deficiency 0.0769233601828955 -2.56494567509068 37 10 0.0598802395209581 167 992 159,2618,7295,2987,2983,471,6240,3614,158,6241 ADSS,GART,TXN,GUK1,GUCY1B1,ATIC,RRM1,IMPDH1,ADSL,RRM2 SMP00167 Adenylosuccinate Lyase Deficiency 0.0769233601828955 -2.56494567509068 37 10 0.0598802395209581 167 992 159,2618,7295,2987,2983,471,6240,3614,158,6241 ADSS,GART,TXN,GUK1,GUCY1B1,ATIC,RRM1,IMPDH1,ADSL,RRM2 SMP00365 Gout or Kelley-Seegmiller Syndrome 0.0769233601828955 -2.56494567509068 37 10 0.0598802395209581 167 992 159,2618,7295,2987,2983,471,6240,3614,158,6241 ADSS,GART,TXN,GUK1,GUCY1B1,ATIC,RRM1,IMPDH1,ADSL,RRM2 SMP00220 Xanthine Dehydrogenase Deficiency (Xanthinuria) 0.0769233601828955 -2.56494567509068 37 10 0.0598802395209581 167 992 159,2618,7295,2987,2983,471,6240,3614,158,6241 ADSS,GART,TXN,GUK1,GUCY1B1,ATIC,RRM1,IMPDH1,ADSL,RRM2 SMP00537 Myoadenylate deaminase deficiency 0.0769233601828955 -2.56494567509068 37 10 0.0598802395209581 167 992 159,2618,7295,2987,2983,471,6240,3614,158,6241 ADSS,GART,TXN,GUK1,GUCY1B1,ATIC,RRM1,IMPDH1,ADSL,RRM2 SMP00050 Purine Metabolism 0.0769233601828955 -2.56494567509068 37 10 0.0598802395209581 167 992 159,2618,7295,2987,2983,471,6240,3614,158,6241 ADSS,GART,TXN,GUK1,GUCY1B1,ATIC,RRM1,IMPDH1,ADSL,RRM2 SMP00144 Adenosine Deaminase Deficiency 0.0769233601828955 -2.56494567509068 37 10 0.0598802395209581 167 992 159,2618,7295,2987,2983,471,6240,3614,158,6241 ADSS,GART,TXN,GUK1,GUCY1B1,ATIC,RRM1,IMPDH1,ADSL,RRM2 SMP00536 Mitochondrial DNA depletion syndrome 0.0769233601828955 -2.56494567509068 37 10 0.0598802395209581 167 992 159,2618,7295,2987,2983,471,6240,3614,158,6241 ADSS,GART,TXN,GUK1,GUCY1B1,ATIC,RRM1,IMPDH1,ADSL,RRM2 SMP00535 Adenine phosphoribosyltransferase deficiency (APRT) 0.0769233601828955 -2.56494567509068 37 10 0.0598802395209581 167 992 159,2618,7295,2987,2983,471,6240,3614,158,6241 ADSS,GART,TXN,GUK1,GUCY1B1,ATIC,RRM1,IMPDH1,ADSL,RRM2 SMP00512 Xanthinuria type I 0.0769233601828955 -2.56494567509068 37 10 0.0598802395209581 167 992 159,2618,7295,2987,2983,471,6240,3614,158,6241 ADSS,GART,TXN,GUK1,GUCY1B1,ATIC,RRM1,IMPDH1,ADSL,RRM2 SMP00513 Xanthinuria type II 0.0769233601828955 -2.56494567509068 37 10 0.0598802395209581 167 992 159,2618,7295,2987,2983,471,6240,3614,158,6241 ADSS,GART,TXN,GUK1,GUCY1B1,ATIC,RRM1,IMPDH1,ADSL,RRM2 SMP00210 Purine Nucleoside Phosphorylase Deficiency 0.0769233601828955 -2.56494567509068 37 10 0.0598802395209581 167 992 159,2618,7295,2987,2983,471,6240,3614,158,6241 ADSS,GART,TXN,GUK1,GUCY1B1,ATIC,RRM1,IMPDH1,ADSL,RRM2 SMP00364 Lesch-Nyhan Syndrome (LNS) 0.0769233601828955 -2.56494567509068 37 10 0.0598802395209581 167 992 159,2618,7295,2987,2983,471,6240,3614,158,6241 ADSS,GART,TXN,GUK1,GUCY1B1,ATIC,RRM1,IMPDH1,ADSL,RRM2 SMP00168 AICA-Ribosiduria 0.0769233601828955 -2.56494567509068 37 10 0.0598802395209581 167 992 159,2618,7295,2987,471,2983,6240,3614,6241,158 ADSS,GART,TXN,GUK1,ATIC,GUCY1B1,RRM1,IMPDH1,RRM2,ADSL SMP00029 Selenoamino Acid Metabolism 0.0972993750819632 -2.32996271240111 11 4 0.0239520958083832 167 992 27430,22928,191,4144 MAT2B,SEPHS2,AHCY,MAT2A SMP00054 Fatty Acid Elongation In Mitochondria 0.097439167010249 -2.32852702380248 7 3 0.0179640718562874 167 992 5538,51102,3032 PPT1,MECR,HADHB SMP00544 Long-chain-3-hydroxyacyl-coa dehydrogenase deficiency (LCHAD) 0.097439167010249 -2.32852702380248 7 3 0.0179640718562874 167 992 5538,51102,3032 PPT1,MECR,HADHB SMP00060 Pyruvate Metabolism 0.125707937087678 -2.07379402227932 21 6 0.0359281437125748 167 992 38,231,4190,2739,3029,97 ACAT1,AKR1B1,MDH1,GLO1,HAGH,ACYP1 SMP00334 Pyruvate Decarboxylase E1 Component Deficiency (PDHE1 Deficiency) 0.125707937087678 -2.07379402227932 21 6 0.0359281437125748 167 992 38,231,4190,2739,97,3029 ACAT1,AKR1B1,MDH1,GLO1,ACYP1,HAGH SMP00196 Leigh Syndrome 0.125707937087678 -2.07379402227932 21 6 0.0359281437125748 167 992 38,231,4190,2739,3029,97 ACAT1,AKR1B1,MDH1,GLO1,HAGH,ACYP1 SMP00212 Pyruvate Dehydrogenase Complex Deficiency 0.125707937087678 -2.07379402227932 21 6 0.0359281437125748 167 992 38,231,4190,2739,97,3029 ACAT1,AKR1B1,MDH1,GLO1,ACYP1,HAGH SMP00558 Primary hyperoxaluria II- PH2 0.125707937087678 -2.07379402227932 21 6 0.0359281437125748 167 992 38,231,4190,2739,97,3029 ACAT1,AKR1B1,MDH1,GLO1,ACYP1,HAGH SMP00559 Pyruvate kinase deficiency 0.125707937087678 -2.07379402227932 21 6 0.0359281437125748 167 992 38,231,4190,2739,97,3029 ACAT1,AKR1B1,MDH1,GLO1,ACYP1,HAGH SMP00127 Glucose-Alanine Cycle 0.13722419910406 -1.9861392009337 8 3 0.0179640718562874 167 992 79751,2746,6509 SLC25A22,GLUD1,SLC1A4 SMP00136 2-Hydroxyglutric Aciduria (D And L Form) 0.149901769535835 -1.89777506916785 22 6 0.0359281437125748 167 992 2746,2730,55191,64841,2806,5859 GLUD1,GCLM,NADSYN1,GNPNAT1,GOT2,QARS SMP00567 Succinic semialdehyde dehydrogenase deficiency 0.149901769535835 -1.89777506916785 22 6 0.0359281437125748 167 992 2730,55191,2746,64841,2806,5859 GCLM,NADSYN1,GLUD1,GNPNAT1,GOT2,QARS SMP00339 Hyperinsulinism-Hyperammonemia Syndrome 0.149901769535835 -1.89777506916785 22 6 0.0359281437125748 167 992 2746,2730,55191,64841,2806,5859 GLUD1,GCLM,NADSYN1,GNPNAT1,GOT2,QARS SMP00243 4-Hydroxybutyric Aciduria/Succinic Semialdehyde Dehydrogenase Deficiency 0.149901769535835 -1.89777506916785 22 6 0.0359281437125748 167 992 2746,2730,55191,64841,2806,5859 GLUD1,GCLM,NADSYN1,GNPNAT1,GOT2,QARS SMP00385 Homocarnosinosis 0.149901769535835 -1.89777506916785 22 6 0.0359281437125748 167 992 2746,2730,55191,64841,2806,5859 GLUD1,GCLM,NADSYN1,GNPNAT1,GOT2,QARS SMP00072 Glutamate Metabolism 0.149901769535835 -1.89777506916785 22 6 0.0359281437125748 167 992 2746,2730,55191,64841,2806,5859 GLUD1,GCLM,NADSYN1,GNPNAT1,GOT2,QARS SMP00358 Fc Epsilon Receptor I Signaling in Mast Cells 0.154553944573201 -1.86721208777145 32 8 0.0479041916167665 167 992 4893,5894,5879,3845,1432,5594,5605,3265 NRAS,RAF1,RAC1,KRAS,MAPK14,MAPK1,MAP2K2,HRAS SMP02313 sarcosine oncometabolite pathway 0.161119042184421 -1.82561179476378 13 4 0.0239520958083832 167 992 27430,4548,4144,23446 MAT2B,MTR,MAT2A,SLC44A1 SMP00002 Carbamoyl Phosphate Synthetase Deficiency 0.161119042184421 -1.82561179476378 13 4 0.0239520958083832 167 992 8604,2746,6509,2806 SLC25A12,GLUD1,SLC1A4,GOT2 SMP00003 Argininosuccinic Aciduria 0.161119042184421 -1.82561179476378 13 4 0.0239520958083832 167 992 8604,2746,6509,2806 SLC25A12,GLUD1,SLC1A4,GOT2 SMP00043 Galactose Metabolism 0.161119042184421 -1.82561179476378 13 4 0.0239520958083832 167 992 2683,231,2584,7360 B4GALT1,AKR1B1,GALK1,UGP2 SMP00205 Ornithine Transcarbamylase Deficiency (OTC Deficiency) 0.161119042184421 -1.82561179476378 13 4 0.0239520958083832 167 992 8604,2746,6509,2806 SLC25A12,GLUD1,SLC1A4,GOT2 SMP00357 Argininemia 0.161119042184421 -1.82561179476378 13 4 0.0239520958083832 167 992 8604,2746,6509,2806 SLC25A12,GLUD1,SLC1A4,GOT2 SMP00182 Galactosemia 0.161119042184421 -1.82561179476378 13 4 0.0239520958083832 167 992 2683,231,2584,7360 B4GALT1,AKR1B1,GALK1,UGP2 SMP00001 Citrullinemia Type I 0.161119042184421 -1.82561179476378 13 4 0.0239520958083832 167 992 8604,2746,6509,2806 SLC25A12,GLUD1,SLC1A4,GOT2 SMP00059 Urea Cycle 0.161119042184421 -1.82561179476378 13 4 0.0239520958083832 167 992 8604,2746,6509,2806 SLC25A12,GLUD1,SLC1A4,GOT2 SMP00219 UMP Synthase Deiciency (Orotic Aciduria) 0.176014676140716 -1.73718790025734 23 6 0.0359281437125748 167 992 124583,6241,1635,7083,1854,1503 CANT1,RRM2,DCTD,TK1,DUT,CTPS1 SMP00202 MNGIE (Mitochondrial Neurogastrointestinal Encephalopathy) 0.176014676140716 -1.73718790025734 23 6 0.0359281437125748 167 992 124583,6241,1635,7083,1854,1503 CANT1,RRM2,DCTD,TK1,DUT,CTPS1 SMP00172 Beta Ureidopropionase Deficiency 0.176014676140716 -1.73718790025734 23 6 0.0359281437125748 167 992 124583,6241,1635,7083,1854,1503 CANT1,RRM2,DCTD,TK1,DUT,CTPS1 SMP00046 Pyrimidine Metabolism 0.176014676140716 -1.73718790025734 23 6 0.0359281437125748 167 992 124583,6241,1635,7083,1854,1503 CANT1,RRM2,DCTD,TK1,DUT,CTPS1 SMP00178 Dihydropyrimidinase Deficiency 0.176014676140716 -1.73718790025734 23 6 0.0359281437125748 167 992 124583,6241,1635,7083,1854,1503 CANT1,RRM2,DCTD,TK1,DUT,CTPS1 SMP00198 Malonic Aciduria 0.19752191793512 -1.62190572391176 14 4 0.0239520958083832 167 992 38,23417,34,4594 ACAT1,MLYCD,ACADM,MUT SMP00201 Methylmalonic Aciduria Due to Cobalamin-Related Disorders 0.19752191793512 -1.62190572391176 14 4 0.0239520958083832 167 992 23417,38,34,4594 MLYCD,ACAT1,ACADM,MUT SMP00502 Malonyl-coa decarboxylase deficiency 0.19752191793512 -1.62190572391176 14 4 0.0239520958083832 167 992 23417,38,34,4594 MLYCD,ACAT1,ACADM,MUT SMP00016 Propanoate Metabolism 0.19752191793512 -1.62190572391176 14 4 0.0239520958083832 167 992 38,23417,34,4594 ACAT1,MLYCD,ACADM,MUT SMP00503 Hypophosphatasia 0.199171744245464 -1.61358779005007 5 2 0.0119760479041916 167 992 57026,8566 PDXP,PDXK SMP00017 Vitamin B6 Metabolism 0.199171744245464 -1.61358779005007 5 2 0.0119760479041916 167 992 57026,8566 PDXP,PDXK SMP00569 Succinyl CoA: 3-ketoacid CoA transferase deficiency 0.199171744245464 -1.61358779005007 5 2 0.0119760479041916 167 992 38,622 ACAT1,BDH1 SMP00071 Ketone Body Metabolism 0.199171744245464 -1.61358779005007 5 2 0.0119760479041916 167 992 38,622 ACAT1,BDH1 SMP00355 Mitochondrial Electron Transport Chain 0.203048550443989 -1.59431016378697 19 5 0.029940119760479 167 992 6390,54205,498,506,6389 SDHB,CYCS,ATP5F1A,ATP5F1B,SDHA SMP00609 Mercaptopurine Metabolism Pathway 0.236131028580115 -1.44336842217832 15 4 0.0239520958083832 167 992 3614,2030,5879,10057 IMPDH1,SLC29A1,RAC1,ABCC5 SMP00025 Phospholipid Biosynthesis 0.263662565337606 -1.33308515498105 26 6 0.0359281437125748 167 992 10423,56994,9791,9489,1119,10554 CDIPT,CHPT1,PTDSS1,PGS1,CHKA,AGPAT1 SMP00027 Pantothenate and CoA Biosynthesis 0.267085299529802 -1.32018719770842 6 2 0.0119760479041916 167 992 79717,60490 PPCS,PPCDC SMP00092 Rosuvastatin Action Pathway 0.270721587131598 -1.30666433994997 21 5 0.029940119760479 167 992 9453,10654,50814,2222,10682 GGPS1,PMVK,NSDHL,FDFT1,EBP SMP00508 Cholesteryl ester storage disease 0.270721587131598 -1.30666433994997 21 5 0.029940119760479 167 992 10654,9453,50814,2222,10682 PMVK,GGPS1,NSDHL,FDFT1,EBP SMP00510 Mevalonic aciduria 0.270721587131598 -1.30666433994997 21 5 0.029940119760479 167 992 10654,9453,50814,2222,10682 PMVK,GGPS1,NSDHL,FDFT1,EBP SMP00387 CHILD Syndrome 0.270721587131598 -1.30666433994997 21 5 0.029940119760479 167 992 10654,9453,50814,2222,10682 PMVK,GGPS1,NSDHL,FDFT1,EBP SMP00095 Alendronate Action Pathway 0.270721587131598 -1.30666433994997 21 5 0.029940119760479 167 992 10654,9453,50814,2222,10682 PMVK,GGPS1,NSDHL,FDFT1,EBP SMP00107 Zoledronate Action Pathway 0.270721587131598 -1.30666433994997 21 5 0.029940119760479 167 992 10654,9453,50814,2222,10682 PMVK,GGPS1,NSDHL,FDFT1,EBP SMP00389 Smith-Lemli-Opitz Syndrome (SLOS) 0.270721587131598 -1.30666433994997 21 5 0.029940119760479 167 992 10654,9453,50814,2222,10682 PMVK,GGPS1,NSDHL,FDFT1,EBP SMP00112 Risedronate Action Pathway 0.270721587131598 -1.30666433994997 21 5 0.029940119760479 167 992 10654,9453,50814,2222,10682 PMVK,GGPS1,NSDHL,FDFT1,EBP SMP00119 Fluvastatin Action Pathway 0.270721587131598 -1.30666433994997 21 5 0.029940119760479 167 992 9453,10654,50814,2222,10682 GGPS1,PMVK,NSDHL,FDFT1,EBP SMP00079 Ibandronate Action Pathway 0.270721587131598 -1.30666433994997 21 5 0.029940119760479 167 992 10654,9453,50814,2222,10682 PMVK,GGPS1,NSDHL,FDFT1,EBP SMP00209 Hypercholesterolemia 0.270721587131598 -1.30666433994997 21 5 0.029940119760479 167 992 10654,9453,50814,2222,10682 PMVK,GGPS1,NSDHL,FDFT1,EBP SMP00388 Chondrodysplasia Punctata II- X Linked Dominant (CDPX2) 0.270721587131598 -1.30666433994997 21 5 0.029940119760479 167 992 10654,9453,50814,2222,10682 PMVK,GGPS1,NSDHL,FDFT1,EBP SMP00386 Desmosterolosis 0.270721587131598 -1.30666433994997 21 5 0.029940119760479 167 992 10654,9453,50814,2222,10682 PMVK,GGPS1,NSDHL,FDFT1,EBP SMP00511 Wolman disease 0.270721587131598 -1.30666433994997 21 5 0.029940119760479 167 992 10654,9453,50814,2222,10682 PMVK,GGPS1,NSDHL,FDFT1,EBP SMP00023 Steroid Biosynthesis 0.270721587131598 -1.30666433994997 21 5 0.029940119760479 167 992 10654,9453,50814,2222,10682 PMVK,GGPS1,NSDHL,FDFT1,EBP SMP00099 Lovastatin Action Pathway 0.270721587131598 -1.30666433994997 21 5 0.029940119760479 167 992 9453,10654,50814,2222,10682 GGPS1,PMVK,NSDHL,FDFT1,EBP SMP00509 Hyper-IgD syndrome 0.270721587131598 -1.30666433994997 21 5 0.029940119760479 167 992 10654,9453,50814,2222,10682 PMVK,GGPS1,NSDHL,FDFT1,EBP SMP00131 Atorvastatin Action Pathway 0.270721587131598 -1.30666433994997 21 5 0.029940119760479 167 992 9453,10654,50814,2222,10682 GGPS1,PMVK,NSDHL,FDFT1,EBP SMP00082 Simvastatin Action Pathway 0.270721587131598 -1.30666433994997 21 5 0.029940119760479 167 992 10654,9453,50814,2222,10682 PMVK,GGPS1,NSDHL,FDFT1,EBP SMP00117 Pamidronate Action Pathway 0.270721587131598 -1.30666433994997 21 5 0.029940119760479 167 992 10654,9453,50814,2222,10682 PMVK,GGPS1,NSDHL,FDFT1,EBP SMP00319 Lysosomal Acid Lipase Deficiency (Wolman Disease) 0.270721587131598 -1.30666433994997 21 5 0.029940119760479 167 992 10654,9453,50814,2222,10682 PMVK,GGPS1,NSDHL,FDFT1,EBP SMP00111 Cerivastatin Action Pathway 0.270721587131598 -1.30666433994997 21 5 0.029940119760479 167 992 9453,10654,50814,2222,10682 GGPS1,PMVK,NSDHL,FDFT1,EBP SMP00089 Pravastatin Action Pathway 0.270721587131598 -1.30666433994997 21 5 0.029940119760479 167 992 9453,10654,50814,2222,10682 GGPS1,PMVK,NSDHL,FDFT1,EBP SMP00442 Etoposide Action Pathway 0.359253115036642 -1.02372808311657 18 4 0.0239520958083832 167 992 7155,5479,23753,10130 TOP2B,PPIB,SDF2L1,PDIA6 SMP00649 Lamivudine Metabolism Pathway 0.359253115036642 -1.02372808311657 18 4 0.0239520958083832 167 992 5833,56994,1633,4363 PCYT2,CHPT1,DCK,ABCC1 SMP00601 Etoposide Metabolism Pathway 0.359253115036642 -1.02372808311657 18 4 0.0239520958083832 167 992 7155,5479,23753,10130 TOP2B,PPIB,SDF2L1,PDIA6 SMP00487 Hyperphenylalaniemia due to guanosine triphosphate cyclohydrolase deficiency 0.400850270350088 -0.914167312051372 8 2 0.0119760479041916 167 992 231,6697 AKR1B1,SPR SMP00496 Galactosemia III 0.400850270350088 -0.914167312051372 8 2 0.0119760479041916 167 992 2584,7360 GALK1,UGP2 SMP00005 Pterine Biosynthesis 0.400850270350088 -0.914167312051372 8 2 0.0119760479041916 167 992 231,6697 AKR1B1,SPR SMP00488 Hyperphenylalaninemia due to 6-pyruvoyltetrahydropterin synthase deficiency (ptps) 0.400850270350088 -0.914167312051372 8 2 0.0119760479041916 167 992 231,6697 AKR1B1,SPR SMP00495 Galactosemia II (GALK) 0.400850270350088 -0.914167312051372 8 2 0.0119760479041916 167 992 2584,7360 GALK1,UGP2 SMP00010 Nucleotide Sugars Metabolism 0.400850270350088 -0.914167312051372 8 2 0.0119760479041916 167 992 2584,7360 GALK1,UGP2 SMP00481 Mitochondrial Beta-Oxidation of Medium Chain Saturated Fatty Acids 0.400850270350088 -0.914167312051372 8 2 0.0119760479041916 167 992 34,3032 ACADM,HADHB SMP00490 Segawa syndrome 0.400850270350088 -0.914167312051372 8 2 0.0119760479041916 167 992 231,6697 AKR1B1,SPR SMP00491 Sepiapterin reductase deficiency 0.400850270350088 -0.914167312051372 8 2 0.0119760479041916 167 992 231,6697 AKR1B1,SPR SMP00486 Dopa-responsive dystonia 0.400850270350088 -0.914167312051372 8 2 0.0119760479041916 167 992 231,6697 AKR1B1,SPR SMP00489 Hyperphenylalaninemia due to dhpr-deficiency 0.400850270350088 -0.914167312051372 8 2 0.0119760479041916 167 992 231,6697 AKR1B1,SPR SMP00619 Felodipine Metabolism Pathway 0.425142139469296 -0.855331720162146 3 1 0.00598802395209581 167 992 782 CACNB1 SMP00185 Glutaric Aciduria Type I 0.427764053363298 -0.849183512598035 14 3 0.0179640718562874 167 992 38,34,3032 ACAT1,ACADM,HADHB SMP00540 Very-long-chain acyl coa dehydrogenase deficiency (VLCAD) 0.427764053363298 -0.849183512598035 14 3 0.0179640718562874 167 992 38,34,3032 ACAT1,ACADM,HADHB SMP00545 Trifunctional protein deficiency 0.427764053363298 -0.849183512598035 14 3 0.0179640718562874 167 992 38,34,3032 ACAT1,ACADM,HADHB SMP00648 Sorafenib Metabolism Pathway 0.427764053363298 -0.849183512598035 14 3 0.0179640718562874 167 992 5479,23753,10130 PPIB,SDF2L1,PDIA6 SMP00542 Medium chain acyl-coa dehydrogenase deficiency (MCAD) 0.427764053363298 -0.849183512598035 14 3 0.0179640718562874 167 992 38,34,3032 ACAT1,ACADM,HADHB SMP00235 Short Chain Acyl CoA Dehydrogenase Deficiency (SCAD Deficiency) 0.427764053363298 -0.849183512598035 14 3 0.0179640718562874 167 992 38,34,3032 ACAT1,ACADM,HADHB SMP00181 Ethylmalonic Encephalopathy 0.427764053363298 -0.849183512598035 14 3 0.0179640718562874 167 992 38,34,3032 ACAT1,ACADM,HADHB SMP00538 Carnitine palmitoyl transferase deficiency (I) 0.427764053363298 -0.849183512598035 14 3 0.0179640718562874 167 992 38,34,3032 ACAT1,ACADM,HADHB SMP00541 Carnitine palmitoyl transferase deficiency (II) 0.427764053363298 -0.849183512598035 14 3 0.0179640718562874 167 992 38,34,3032 ACAT1,ACADM,HADHB SMP00051 Fatty acid Metabolism 0.427764053363298 -0.849183512598035 14 3 0.0179640718562874 167 992 38,34,3032 ACAT1,ACADM,HADHB SMP00539 Long chain acyl-CoA dehydrogenase deficiency (LCAD) 0.427764053363298 -0.849183512598035 14 3 0.0179640718562874 167 992 38,34,3032 ACAT1,ACADM,HADHB SMP00335 Intracellular Signalling Through Histamine H2 Receptor and Histamine 0.463541836073662 -0.768858636833426 9 2 0.0119760479041916 167 992 2778,1385 GNAS,CREB1 SMP00333 Intracellular Signalling Through FSH Receptor and Follicle Stimulating Hormone 0.463541836073662 -0.768858636833426 9 2 0.0119760479041916 167 992 2778,1385 GNAS,CREB1 SMP00312 Excitatory Neural Signalling Through 5-HTR 6 and Serotonin 0.463541836073662 -0.768858636833426 9 2 0.0119760479041916 167 992 2778,1385 GNAS,CREB1 SMP00309 Excitatory Neural Signalling Through 5-HTR 4 and Serotonin 0.463541836073662 -0.768858636833426 9 2 0.0119760479041916 167 992 2778,1385 GNAS,CREB1 SMP00311 Excitatory Neural Signalling Through 5-HTR 7 and Serotonin 0.463541836073662 -0.768858636833426 9 2 0.0119760479041916 167 992 2778,1385 GNAS,CREB1 SMP00622 Morphine Metabolism Pathway 0.475672309560162 -0.743026087117998 15 3 0.0179640718562874 167 992 5479,23753,10130 PPIB,SDF2L1,PDIA6 SMP00345 Congenital Erythropoietic Porphyria (CEP) or Gunther Disease 0.475672309560162 -0.743026087117998 15 3 0.0179640718562874 167 992 1355,1371,7389 COX15,CPOX,UROD SMP00518 Glucose-6-phosphate dehydrogenase deficiency 0.475672309560162 -0.743026087117998 15 3 0.0179640718562874 167 992 2821,6888,7086 GPI,TALDO1,TKT SMP00031 Pentose Phosphate Pathway 0.475672309560162 -0.743026087117998 15 3 0.0179640718562874 167 992 2821,6888,7086 GPI,TALDO1,TKT SMP00344 Acute Intermittent Porphyria 0.475672309560162 -0.743026087117998 15 3 0.0179640718562874 167 992 1355,1371,7389 COX15,CPOX,UROD SMP00024 Porphyrin Metabolism 0.475672309560162 -0.743026087117998 15 3 0.0179640718562874 167 992 1355,1371,7389 COX15,CPOX,UROD SMP00342 Hereditary Coproporphyria (HCP) 0.475672309560162 -0.743026087117998 15 3 0.0179640718562874 167 992 1355,1371,7389 COX15,CPOX,UROD SMP00519 Ribose-5-phosphate isomerase deficiency 0.475672309560162 -0.743026087117998 15 3 0.0179640718562874 167 992 2821,6888,7086 GPI,TALDO1,TKT SMP00346 Porphyria Variegata (PV) 0.475672309560162 -0.743026087117998 15 3 0.0179640718562874 167 992 1355,1371,7389 COX15,CPOX,UROD SMP00520 Transaldolase deficiency 0.475672309560162 -0.743026087117998 15 3 0.0179640718562874 167 992 2821,6888,7086 GPI,TALDO1,TKT SMP00433 Irinotecan Action Pathway 0.482406976675315 -0.728967171245643 21 4 0.0239520958083832 167 992 5479,23753,10130,4363 PPIB,SDF2L1,PDIA6,ABCC1 SMP00600 Irinotecan Metabolism Pathway 0.482406976675315 -0.728967171245643 21 4 0.0239520958083832 167 992 5479,23753,10130,4363 PPIB,SDF2L1,PDIA6,ABCC1 SMP00128 Gluconeogenesis 0.521551454247325 -0.650947343545907 22 4 0.0239520958083832 167 992 2821,5223,4191,51660 GPI,PGAM1,MDH2,MPC1 SMP00581 Glycogenosis- Type IA. Von gierke disease 0.521551454247325 -0.650947343545907 22 4 0.0239520958083832 167 992 2821,5223,4191,51660 GPI,PGAM1,MDH2,MPC1 SMP00574 Glycogenosis- Type IC 0.521551454247325 -0.650947343545907 22 4 0.0239520958083832 167 992 2821,5223,4191,51660 GPI,PGAM1,MDH2,MPC1 SMP00563 Triosephosphate isomerase 0.521551454247325 -0.650947343545907 22 4 0.0239520958083832 167 992 2821,5223,4191,51660 GPI,PGAM1,MDH2,MPC1 SMP00562 Fructose-1-6-diphosphatase deficiency 0.521551454247325 -0.650947343545907 22 4 0.0239520958083832 167 992 2821,5223,4191,51660 GPI,PGAM1,MDH2,MPC1 SMP00374 Glycogen Storage Disease Type 1A (GSD1A) or Von Gierke Disease 0.521551454247325 -0.650947343545907 22 4 0.0239520958083832 167 992 2821,5223,4191,51660 GPI,PGAM1,MDH2,MPC1 SMP00560 Phosphoenolpyruvate carboxykinase deficiency 1 (PEPCK1) 0.521551454247325 -0.650947343545907 22 4 0.0239520958083832 167 992 2821,5223,4191,51660 GPI,PGAM1,MDH2,MPC1 SMP00573 Glycogenosis- Type IB 0.521551454247325 -0.650947343545907 22 4 0.0239520958083832 167 992 2821,5223,4191,51660 GPI,PGAM1,MDH2,MPC1 SMP00640 Acetaminophen Metabolism Pathway 0.521694929468502 -0.650672288248671 28 5 0.029940119760479 167 992 5479,23753,10130,10057,4363 PPIB,SDF2L1,PDIA6,ABCC5,ABCC1 SMP00076 Thiamine Metabolism 0.522211161420729 -0.64968324910269 4 1 0.00598802395209581 167 992 84284 NTPCR SMP00479 Plasmalogen Synthesis 0.522211161420729 -0.64968324910269 4 1 0.00598802395209581 167 992 10554 AGPAT1 SMP00437 Vincristine Action Pathway 0.522231473263178 -0.649644354017833 10 2 0.0119760479041916 167 992 89845,4363 ABCC10,ABCC1 SMP00438 Vindesine Action Pathway 0.522231473263178 -0.649644354017833 10 2 0.0119760479041916 167 992 89845,4363 ABCC10,ABCC1 SMP00338 Intracellular Signalling Through LHCGR Receptor and Luteinizing Hormone/Choriogonadotropin 0.522231473263178 -0.649644354017833 10 2 0.0119760479041916 167 992 2778,1385 GNAS,CREB1 SMP00650 Doxorubicin Metabolism Pathway 0.565409274810027 -0.57020542987766 17 3 0.0179640718562874 167 992 1728,374291,4363 NQO1,NDUFS7,ABCC1 SMP00436 Vinblastine Action Pathway 0.576485188565684 -0.550805631596678 11 2 0.0119760479041916 167 992 89845,4363 ABCC10,ABCC1 SMP00187 Glycerol Kinase Deficiency 0.576485188565684 -0.550805631596678 11 2 0.0119760479041916 167 992 231,10554 AKR1B1,AGPAT1 SMP00439 Vinorelbine Action Pathway 0.576485188565684 -0.550805631596678 11 2 0.0119760479041916 167 992 89845,4363 ABCC10,ABCC1 SMP00009 Ammonia Recycling 0.576485188565684 -0.550805631596678 11 2 0.0119760479041916 167 992 2746,2653 GLUD1,GCSH SMP00530 Familial lipoprotein lipase deficiency 0.576485188565684 -0.550805631596678 11 2 0.0119760479041916 167 992 231,10554 AKR1B1,AGPAT1 SMP00529 D-glyceric acidura 0.576485188565684 -0.550805631596678 11 2 0.0119760479041916 167 992 231,10554 AKR1B1,AGPAT1 SMP00039 Glycerolipid Metabolism 0.576485188565684 -0.550805631596678 11 2 0.0119760479041916 167 992 231,10554 AKR1B1,AGPAT1 SMP00522 3-hydroxyisobutyric aciduria 0.587875963465207 -0.531239299823594 30 5 0.029940119760479 167 992 38,34,27034,4594,56922 ACAT1,ACADM,ACAD8,MUT,MCCC1 SMP00524 Isovaleric acidemia 0.587875963465207 -0.531239299823594 30 5 0.029940119760479 167 992 38,34,27034,4594,56922 ACAT1,ACADM,ACAD8,MUT,MCCC1 SMP00523 Isobutyryl-coa dehydrogenase deficiency 0.587875963465207 -0.531239299823594 30 5 0.029940119760479 167 992 38,34,27034,4594,56922 ACAT1,ACADM,ACAD8,MUT,MCCC1 SMP00237 3-Methylcrotonyl Coa Carboxylase Deficiency Type I 0.587875963465207 -0.531239299823594 30 5 0.029940119760479 167 992 38,34,27034,4594,56922 ACAT1,ACADM,ACAD8,MUT,MCCC1 SMP00238 Isovaleric Aciduria 0.587875963465207 -0.531239299823594 30 5 0.029940119760479 167 992 38,34,27034,4594,56922 ACAT1,ACADM,ACAD8,MUT,MCCC1 SMP00199 Maple Syrup Urine Disease 0.587875963465207 -0.531239299823594 30 5 0.029940119760479 167 992 38,34,27034,4594,56922 ACAT1,ACADM,ACAD8,MUT,MCCC1 SMP00521 3-hydroxyisobutyric acid dehydrogenase deficiency 0.587875963465207 -0.531239299823594 30 5 0.029940119760479 167 992 38,34,27034,4594,56922 ACAT1,ACADM,ACAD8,MUT,MCCC1 SMP00236 Propionic Acidemia 0.587875963465207 -0.531239299823594 30 5 0.029940119760479 167 992 38,34,27034,4594,56922 ACAT1,ACADM,ACAD8,MUT,MCCC1 SMP00200 Methylmalonic Aciduria 0.587875963465207 -0.531239299823594 30 5 0.029940119760479 167 992 38,34,27034,4594,56922 ACAT1,ACADM,ACAD8,MUT,MCCC1 SMP00384 Methylmalonate Semialdehyde Dehydrogenase Deficiency 0.587875963465207 -0.531239299823594 30 5 0.029940119760479 167 992 38,34,27034,4594,56922 ACAT1,ACADM,ACAD8,MUT,MCCC1 SMP00140 3-Methylglutaconic Aciduria Type III 0.587875963465207 -0.531239299823594 30 5 0.029940119760479 167 992 38,34,27034,4594,56922 ACAT1,ACADM,ACAD8,MUT,MCCC1 SMP00139 3-Methylglutaconic Aciduria Type I 0.587875963465207 -0.531239299823594 30 5 0.029940119760479 167 992 38,34,27034,4594,56922 ACAT1,ACADM,ACAD8,MUT,MCCC1 SMP00032 Valine- Leucine and Isoleucine Degradation 0.587875963465207 -0.531239299823594 30 5 0.029940119760479 167 992 38,34,27034,4594,56922 ACAT1,ACADM,ACAD8,MUT,MCCC1 SMP00173 Beta-Ketothiolase Deficiency 0.587875963465207 -0.531239299823594 30 5 0.029940119760479 167 992 38,34,27034,4594,56922 ACAT1,ACADM,ACAD8,MUT,MCCC1 SMP00141 3-Methylglutaconic Aciduria Type IV 0.587875963465207 -0.531239299823594 30 5 0.029940119760479 167 992 38,34,27034,4594,56922 ACAT1,ACADM,ACAD8,MUT,MCCC1 SMP00137 2-Methyl-3-Hydroxybutryl CoA Dehydrogenase Deficiency 0.587875963465207 -0.531239299823594 30 5 0.029940119760479 167 992 38,34,27034,4594,56922 ACAT1,ACADM,ACAD8,MUT,MCCC1 SMP00138 3-Hydroxy-3-Methylglutaryl-CoA Lyase Deficiency 0.587875963465207 -0.531239299823594 30 5 0.029940119760479 167 992 38,34,27034,4594,56922 ACAT1,ACADM,ACAD8,MUT,MCCC1 SMP00070 Riboflavin Metabolism 0.602971015716764 -0.5058861502149 5 1 0.00598802395209581 167 992 80308 FLAD1 SMP00468 Degradation of Superoxides 0.602971015716764 -0.5058861502149 5 1 0.00598802395209581 167 992 847 CAT SMP00021 Taurine and Hypotaurine Metabolism 0.602971015716764 -0.5058861502149 5 1 0.00598802395209581 167 992 84890 ADO SMP00516 Adrenoleukodystrophy- X-linked 0.602971015716764 -0.5058861502149 5 1 0.00598802395209581 167 992 1384 CRAT SMP00454 Repaglinide Action Pathway 0.602971015716764 -0.5058861502149 5 1 0.00598802395209581 167 992 782 CACNB1 SMP00453 Nateglinide Action Pathway 0.602971015716764 -0.5058861502149 5 1 0.00598802395209581 167 992 782 CACNB1 SMP00052 Beta Oxidation of Very Long Chain Fatty Acids 0.602971015716764 -0.5058861502149 5 1 0.00598802395209581 167 992 1384 CRAT SMP00460 Glibenclamide Action Pathway 0.602971015716764 -0.5058861502149 5 1 0.00598802395209581 167 992 782 CACNB1 SMP00018 Alpha Linolenic Acid and Linoleic Acid Metabolism 0.602971015716764 -0.5058861502149 5 1 0.00598802395209581 167 992 60481 ELOVL5 SMP00643 Pancreas Function 0.602971015716764 -0.5058861502149 5 1 0.00598802395209581 167 992 782 CACNB1 SMP00517 Carnitine-acylcarnitine translocase deficiency 0.602971015716764 -0.5058861502149 5 1 0.00598802395209581 167 992 1384 CRAT SMP00310 Corticotropin Activation of Cortisol Production 0.602971015716764 -0.5058861502149 5 1 0.00598802395209581 167 992 2778 GNAS SMP00461 Gliclazide Action Pathway 0.602971015716764 -0.5058861502149 5 1 0.00598802395209581 167 992 782 CACNB1 SMP00465 Carnitine Synthesis 0.602971015716764 -0.5058861502149 5 1 0.00598802395209581 167 992 223 ALDH9A1 SMP00554 Glycogenosis- Type IV. Amylopectinosis 0.626126508499097 -0.468202838045374 12 2 0.0119760479041916 167 992 2821,7360 GPI,UGP2 SMP00553 Glycogenosis- Type III. Cori disease 0.626126508499097 -0.468202838045374 12 2 0.0119760479041916 167 992 2821,7360 GPI,UGP2 SMP00478 Nucleotide Excision Repair 0.670148158956322 -0.400256458272742 6 1 0.00598802395209581 167 992 5426 POLE SMP00343 Intracellular Signalling Through PGD2 receptor and Prostaglandin D2 0.670148158956322 -0.400256458272742 6 1 0.00598802395209581 167 992 2778 GNAS SMP00308 Dopamine Activation of Neurological Reward System 0.670148158956322 -0.400256458272742 6 1 0.00598802395209581 167 992 2778 GNAS SMP00037 Lysine Degradation 0.671162882242814 -0.39874342595003 13 2 0.0119760479041916 167 992 38,55526 ACAT1,DHTKD1 SMP00186 Glutaric Aciduria Type I 0.671162882242814 -0.39874342595003 13 2 0.0119760479041916 167 992 55526,38 DHTKD1,ACAT1 SMP00528 Hyperlysinemia II or Saccharopinuria 0.671162882242814 -0.39874342595003 13 2 0.0119760479041916 167 992 55526,38 DHTKD1,ACAT1 SMP00527 Hyperlysinemia I- Familial 0.671162882242814 -0.39874342595003 13 2 0.0119760479041916 167 992 55526,38 DHTKD1,ACAT1 SMP00239 Saccharopinuria/Hyperlysinemia II 0.671162882242814 -0.39874342595003 13 2 0.0119760479041916 167 992 38,55526 ACAT1,DHTKD1 SMP00719 2-aminoadipic 2-oxoadipic aciduria 0.671162882242814 -0.39874342595003 13 2 0.0119760479041916 167 992 55526,38 DHTKD1,ACAT1 SMP00571 Pyridoxine dependency with seizures 0.671162882242814 -0.39874342595003 13 2 0.0119760479041916 167 992 55526,38 DHTKD1,ACAT1 SMP00363 Ornithine Aminotransferase Deficiency (OAT Deficiency) 0.681061790554868 -0.384102241919623 20 3 0.0179640718562874 167 992 2058,2746,4942 EPRS,GLUD1,OAT SMP00506 Hyperornithinemia-hyperammonemia-homocitrullinuria [HHH-syndrome] 0.681061790554868 -0.384102241919623 20 3 0.0179640718562874 167 992 2058,2746,4942 EPRS,GLUD1,OAT SMP00582 Joubert syndrome 0.681061790554868 -0.384102241919623 20 3 0.0179640718562874 167 992 200576,10423,5305 PIKFYVE,CDIPT,PIP4K2A SMP00507 L-arginine:glycine amidinotransferase deficiency 0.681061790554868 -0.384102241919623 20 3 0.0179640718562874 167 992 2058,2746,4942 EPRS,GLUD1,OAT SMP00505 Hyperornithinemia with gyrate atrophy (HOGA) 0.681061790554868 -0.384102241919623 20 3 0.0179640718562874 167 992 2058,2746,4942 EPRS,GLUD1,OAT SMP00362 Arginine: Glycine Amidinotransferase Deficiency (AGAT Deficiency) 0.681061790554868 -0.384102241919623 20 3 0.0179640718562874 167 992 2058,2746,4942 EPRS,GLUD1,OAT SMP00504 Creatine deficiency- guanidinoacetate methyltransferase deficiency 0.681061790554868 -0.384102241919623 20 3 0.0179640718562874 167 992 2058,2746,4942 EPRS,GLUD1,OAT SMP00207 Prolidase Deficiency (PD) 0.681061790554868 -0.384102241919623 20 3 0.0179640718562874 167 992 2058,2746,4942 EPRS,GLUD1,OAT SMP00360 Hyperprolinemia Type II 0.681061790554868 -0.384102241919623 20 3 0.0179640718562874 167 992 2058,2746,4942 EPRS,GLUD1,OAT SMP00188 Guanidinoacetate Methyltransferase Deficiency (GAMT Deficiency) 0.681061790554868 -0.384102241919623 20 3 0.0179640718562874 167 992 2058,2746,4942 EPRS,GLUD1,OAT SMP00463 Phosphatidylinositol Phosphate Metabolism 0.681061790554868 -0.384102241919623 20 3 0.0179640718562874 167 992 200576,10423,5305 PIKFYVE,CDIPT,PIP4K2A SMP00208 Prolinemia Type II 0.681061790554868 -0.384102241919623 20 3 0.0179640718562874 167 992 2058,2746,4942 EPRS,GLUD1,OAT SMP00361 Hyperprolinemia Type I 0.681061790554868 -0.384102241919623 20 3 0.0179640718562874 167 992 2058,2746,4942 EPRS,GLUD1,OAT SMP00020 Arginine and Proline Metabolism 0.681061790554868 -0.384102241919623 20 3 0.0179640718562874 167 992 2058,2746,4942 EPRS,GLUD1,OAT SMP00462 Inositol Phosphate Metabolism 0.711729353723583 -0.340057561009272 14 2 0.0119760479041916 167 992 9562,11165 MINPP1,NUDT3 SMP00525 Fabry disease 0.714170926201931 -0.336632952852672 21 3 0.0179640718562874 167 992 2581,2629,64781 GALC,GBA,CERK SMP00526 Krabbe disease 0.714170926201931 -0.336632952852672 21 3 0.0179640718562874 167 992 2581,2629,64781 GALC,GBA,CERK SMP00349 Gaucher Disease 0.714170926201931 -0.336632952852672 21 3 0.0179640718562874 167 992 2581,2629,64781 GALC,GBA,CERK SMP00034 Sphingolipid Metabolism 0.714170926201931 -0.336632952852672 21 3 0.0179640718562874 167 992 2581,2629,64781 GALC,GBA,CERK SMP00347 Metachromatic Leukodystrophy (MLD) 0.714170926201931 -0.336632952852672 21 3 0.0179640718562874 167 992 2581,2629,64781 GALC,GBA,CERK SMP00348 Globoid Cell Leukodystrophy 0.714170926201931 -0.336632952852672 21 3 0.0179640718562874 167 992 2581,2629,64781 GALC,GBA,CERK SMP00449 Ethanol Degradation 0.726015560027959 -0.320183831841617 7 1 0.00598802395209581 167 992 847 CAT SMP00434 Paclitaxel Action Pathway 0.726015560027959 -0.320183831841617 7 1 0.00598802395209581 167 992 4363 ABCC1 SMP00322 Vasopressin Regulation of Water Homeostasis 0.726015560027959 -0.320183831841617 7 1 0.00598802395209581 167 992 2778 GNAS SMP00682 Leucine Stimulation on Insulin Signaling 0.726015560027959 -0.320183831841617 7 1 0.00598802395209581 167 992 6009 RHEB SMP00435 Docetaxel Action Pathway 0.726015560027959 -0.320183831841617 7 1 0.00598802395209581 167 992 4363 ABCC1 SMP00590 Ibuprofen Metabolism Pathway 0.744584527036794 -0.294928897994735 22 3 0.0179640718562874 167 992 5479,23753,10130 PPIB,SDF2L1,PDIA6 SMP00040 Glycolysis 0.748045822057872 -0.290291043448285 15 2 0.0119760479041916 167 992 2821,5223 GPI,PGAM1 SMP00531 Glycogenosis- Type VII. Tarui disease 0.748045822057872 -0.290291043448285 15 2 0.0119760479041916 167 992 2821,5223 GPI,PGAM1 SMP00572 Fanconi-bickel syndrome 0.748045822057872 -0.290291043448285 15 2 0.0119760479041916 167 992 2821,5223 GPI,PGAM1 SMP00030 Oxidation of Branched Chain Fatty Acids 0.772467744269199 -0.258165026073328 8 1 0.00598802395209581 167 992 1384 CRAT SMP00073 Butyrate Metabolism 0.772467744269199 -0.258165026073328 8 1 0.00598802395209581 167 992 38 ACAT1 SMP00480 Mitochondrial Beta-Oxidation of Short Chain Saturated Fatty Acids 0.772467744269199 -0.258165026073328 8 1 0.00598802395209581 167 992 38 ACAT1 SMP00568 Short-chain 3-hydroxyacyl-CoA dehydrogenase deficiency (SCHAD) 0.772467744269199 -0.258165026073328 8 1 0.00598802395209581 167 992 38 ACAT1 SMP00354 Intracellular Signalling Through Prostacyclin Receptor and Prostacyclin 0.772467744269199 -0.258165026073328 8 1 0.00598802395209581 167 992 2778 GNAS SMP00642 Nevirapine Metabolism Pathway 0.772467744269199 -0.258165026073328 8 1 0.00598802395209581 167 992 89845 ABCC10 SMP00555 Glycogenosis- Type VI. Hers disease 0.780384949438118 -0.247967956121205 16 2 0.0119760479041916 167 992 2821,7360 GPI,UGP2 SMP00058 Starch and Sucrose Metabolism 0.780384949438118 -0.247967956121205 16 2 0.0119760479041916 167 992 2821,7360 GPI,UGP2 SMP00557 Sucrase-isomaltase deficiency 0.780384949438118 -0.247967956121205 16 2 0.0119760479041916 167 992 2821,7360 GPI,UGP2 SMP00556 Mucopolysaccharidosis VI. Sly syndrome 0.780384949438118 -0.247967956121205 16 2 0.0119760479041916 167 992 2821,7360 GPI,UGP2 SMP00552 Glycogen synthetase deficiency 0.780384949438118 -0.247967956121205 16 2 0.0119760479041916 167 992 2821,7360 GPI,UGP2 SMP00499 Beta-mercaptolactate-cysteine disulfiduria 0.811083482795136 -0.209384292069374 9 1 0.00598802395209581 167 992 2730 GCLM SMP00013 Cysteine Metabolism 0.811083482795136 -0.209384292069374 9 1 0.00598802395209581 167 992 2730 GCLM SMP00452 Threonine and 2-Oxobutanoate Degradation 0.811083482795136 -0.209384292069374 9 1 0.00598802395209581 167 992 4594 MUT SMP00722 Cystinosis- ocular nonnephropathic 0.811083482795136 -0.209384292069374 9 1 0.00598802395209581 167 992 2730 GCLM SMP00406 Morphine Action Pathway 0.83197436666585 -0.183953647931398 40 5 0.029940119760479 167 992 782,5479,476,23753,10130 CACNB1,PPIB,ATP1A1,SDF2L1,PDIA6 SMP00725 Fructose intolerance- hereditary 0.834349355968247 -0.181103072285913 18 2 0.0119760479041916 167 992 231,7264 AKR1B1,TSTA3 SMP00561 Fructosuria 0.834349355968247 -0.181103072285913 18 2 0.0119760479041916 167 992 231,7264 AKR1B1,TSTA3 SMP00064 Fructose and Mannose Degradation 0.834349355968247 -0.181103072285913 18 2 0.0119760479041916 167 992 231,7264 AKR1B1,TSTA3 SMP00482 Mitochondrial Beta-Oxidation of Long Chain Saturated Fatty Acids 0.843178150522931 -0.170577014098457 10 1 0.00598802395209581 167 992 3032 HADHB SMP00336 Vitamin A Deficiency 0.867718430660034 -0.141888005587677 35 4 0.0239520958083832 167 992 5479,23753,10130,51109 PPIB,SDF2L1,PDIA6,RDH11 SMP00074 Retinol Metabolism 0.867718430660034 -0.141888005587677 35 4 0.0239520958083832 167 992 5479,23753,10130,51109 PPIB,SDF2L1,PDIA6,RDH11 SMP00015 Glutathione Metabolism 0.86984744672098 -0.139437431305445 11 1 0.00598802395209581 167 992 2730 GCLM SMP00500 5-oxoprolinase deficiency 0.86984744672098 -0.139437431305445 11 1 0.00598802395209581 167 992 2730 GCLM SMP00635 Valproic Acid Metabolism Pathway 0.86984744672098 -0.139437431305445 11 1 0.00598802395209581 167 992 3032 HADHB SMP00370 Tyrosinemia Type 3 (TYRO3) 0.86984744672098 -0.139437431305445 11 1 0.00598802395209581 167 992 2193 FARSA SMP00008 Phenylalanine and Tyrosine Metabolism 0.86984744672098 -0.139437431305445 11 1 0.00598802395209581 167 992 2193 FARSA SMP00337 Glutathione Synthetase Deficiency 0.86984744672098 -0.139437431305445 11 1 0.00598802395209581 167 992 2730 GCLM SMP00143 5-Oxoprolinuria 0.86984744672098 -0.139437431305445 11 1 0.00598802395209581 167 992 2730 GCLM SMP00501 Gamma-glutamyl-transpeptidase deficiency 0.86984744672098 -0.139437431305445 11 1 0.00598802395209581 167 992 2730 GCLM SMP00206 Phenylketonuria 0.86984744672098 -0.139437431305445 11 1 0.00598802395209581 167 992 2193 FARSA SMP00183 Gamma-Glutamyltransferase Deficiency 0.86984744672098 -0.139437431305445 11 1 0.00598802395209581 167 992 2730 GCLM SMP00369 Tyrosinemia Type 2 (or Richner-Hanhart syndrome) 0.86984744672098 -0.139437431305445 11 1 0.00598802395209581 167 992 2193 FARSA SMP00543 Methylenetetrahydrofolate Reductase Deficiency (MTHFRD) 0.892003895651131 -0.114284779089769 12 1 0.00598802395209581 167 992 10797 MTHFD2 SMP00053 Folate Metabolism 0.892003895651131 -0.114284779089769 12 1 0.00598802395209581 167 992 10797 MTHFD2 SMP00432 Methotrexate Action Pathway 0.892003895651131 -0.114284779089769 12 1 0.00598802395209581 167 992 10797 MTHFD2 SMP00494 Tyrosinemia- transient 0.892003895651131 -0.114284779089769 12 1 0.00598802395209581 167 992 4282 MIF SMP00724 Folate malabsorption- hereditary 0.892003895651131 -0.114284779089769 12 1 0.00598802395209581 167 992 10797 MTHFD2 SMP00458 Lactose Intolerance 0.892003895651131 -0.114284779089769 12 1 0.00598802395209581 167 992 476 ATP1A1 SMP00457 Lactose Degradation 0.892003895651131 -0.114284779089769 12 1 0.00598802395209581 167 992 476 ATP1A1 SMP00011 Inositol Metabolism 0.893150358993403 -0.11300033714655 21 2 0.0119760479041916 167 992 9562,200576 MINPP1,PIKFYVE SMP00467 Trehalose Degradation 0.910407313437001 -0.0938631824294624 13 1 0.00598802395209581 167 992 476 ATP1A1 SMP00086 Ibuprofen Action Pathway 0.920673601611381 -0.082649701184345 47 5 0.029940119760479 167 992 5479,23753,4048,10130,2053 PPIB,SDF2L1,LTA4H,PDIA6,EPHX2 SMP00282 Streptokinase Action Pathway 0.925690233416448 -0.0772156214491829 14 1 0.00598802395209581 167 992 79001 VKORC1 SMP00268 Warfarin Action Pathway 0.925690233416448 -0.0772156214491829 14 1 0.00598802395209581 167 992 79001 VKORC1 SMP00276 Argatroban Action Pathway 0.925690233416448 -0.0772156214491829 14 1 0.00598802395209581 167 992 79001 VKORC1 SMP00288 Aprotinin Action Pathway 0.925690233416448 -0.0772156214491829 14 1 0.00598802395209581 167 992 79001 VKORC1 SMP00279 Ximelagatran Action Pathway 0.925690233416448 -0.0772156214491829 14 1 0.00598802395209581 167 992 79001 VKORC1 SMP00281 Anistreplase Action Pathway 0.925690233416448 -0.0772156214491829 14 1 0.00598802395209581 167 992 79001 VKORC1 SMP00656 Dicoumarol Action Pathway 0.925690233416448 -0.0772156214491829 14 1 0.00598802395209581 167 992 79001 VKORC1 SMP00048 Nicotinate and Nicotinamide Metabolism 0.925690233416448 -0.0772156214491829 14 1 0.00598802395209581 167 992 55191 NADSYN1 SMP00283 Tenecteplase Action Pathway 0.925690233416448 -0.0772156214491829 14 1 0.00598802395209581 167 992 79001 VKORC1 SMP00269 Acenocoumarol Action Pathway 0.925690233416448 -0.0772156214491829 14 1 0.00598802395209581 167 992 79001 VKORC1 SMP00280 Alteplase Action Pathway 0.925690233416448 -0.0772156214491829 14 1 0.00598802395209581 167 992 79001 VKORC1 SMP00277 Bivalirudin Action Pathway 0.925690233416448 -0.0772156214491829 14 1 0.00598802395209581 167 992 79001 VKORC1 SMP00271 Phenprocoumon Action Pathway 0.925690233416448 -0.0772156214491829 14 1 0.00598802395209581 167 992 79001 VKORC1 SMP00044 Histidine Metabolism 0.925690233416448 -0.0772156214491829 14 1 0.00598802395209581 167 992 3035 HARS SMP00285 Reteplase Action Pathway 0.925690233416448 -0.0772156214491829 14 1 0.00598802395209581 167 992 79001 VKORC1 SMP00191 Histidinemia 0.925690233416448 -0.0772156214491829 14 1 0.00598802395209581 167 992 3035 HARS SMP00278 Lepirudin Action Pathway 0.925690233416448 -0.0772156214491829 14 1 0.00598802395209581 167 992 79001 VKORC1 SMP00655 Phenindione Action Pathway 0.925690233416448 -0.0772156214491829 14 1 0.00598802395209581 167 992 79001 VKORC1 SMP00586 Coagulation 0.925690233416448 -0.0772156214491829 14 1 0.00598802395209581 167 992 79001 VKORC1 SMP00284 Urokinase Action Pathway 0.925690233416448 -0.0772156214491829 14 1 0.00598802395209581 167 992 79001 VKORC1 SMP00287 Tranexamic Acid Action Pathway 0.925690233416448 -0.0772156214491829 14 1 0.00598802395209581 167 992 79001 VKORC1 SMP00067 Aspartate Metabolism 0.925690233416448 -0.0772156214491829 14 1 0.00598802395209581 167 992 158 ADSL SMP00270 Dicumarol Action Pathway 0.925690233416448 -0.0772156214491829 14 1 0.00598802395209581 167 992 79001 VKORC1 SMP00175 Canavan Disease 0.925690233416448 -0.0772156214491829 14 1 0.00598802395209581 167 992 158 ADSL SMP00192 Hypoacetylaspartia 0.925690233416448 -0.0772156214491829 14 1 0.00598802395209581 167 992 158 ADSL SMP00286 Aminocaproic Acid Action Pathway 0.925690233416448 -0.0772156214491829 14 1 0.00598802395209581 167 992 79001 VKORC1 SMP00327 Phenytoin (Antiarrhythmic) Action Pathway 0.92686272848636 -0.0759498058416611 77 9 0.0538922155688623 167 992 782,5479,476,488,1728,23753,3784,5566,10130 CACNB1,PPIB,ATP1A1,ATP2A2,NQO1,SDF2L1,KCNQ1,PRKACA,PDIA6 SMP00429 Disulfiram Action Pathway 0.932127769045829 -0.070285382441803 24 2 0.0119760479041916 167 992 847,4282 CAT,MIF SMP00275 Ardeparin Action Pathway 0.938379119944471 -0.0636012325889827 15 1 0.00598802395209581 167 992 79001 VKORC1 SMP00273 Fondaparinux Action Pathway 0.938379119944471 -0.0636012325889827 15 1 0.00598802395209581 167 992 79001 VKORC1 SMP00274 Heparin Action Pathway 0.938379119944471 -0.0636012325889827 15 1 0.00598802395209581 167 992 79001 VKORC1 SMP00272 Enoxaparin Action Pathway 0.938379119944471 -0.0636012325889827 15 1 0.00598802395209581 167 992 79001 VKORC1 SMP00652 Mycophenolic Acid Metabolism Pathway 0.948912064646196 -0.0524391457337974 16 1 0.00598802395209581 167 992 3614 IMPDH1 SMP00674 Anileridine Action Pathway 0.950205179234751 -0.0510773395656286 26 2 0.0119760479041916 167 992 782,476 CACNB1,ATP1A1 SMP00411 Hydrocodone Action Pathway 0.950205179234751 -0.0510773395656286 26 2 0.0119760479041916 167 992 782,476 CACNB1,ATP1A1 SMP00689 Dihydromorphine Action Pathway 0.950205179234751 -0.0510773395656286 26 2 0.0119760479041916 167 992 782,476 CACNB1,ATP1A1 SMP00687 Naltrexone Action Pathway 0.950205179234751 -0.0510773395656286 26 2 0.0119760479041916 167 992 782,476 CACNB1,ATP1A1 SMP00675 Diphenoxylate Action Pathway 0.950205179234751 -0.0510773395656286 26 2 0.0119760479041916 167 992 782,476 CACNB1,ATP1A1 SMP00417 Sufentanil Action Pathway 0.950205179234751 -0.0510773395656286 26 2 0.0119760479041916 167 992 782,476 CACNB1,ATP1A1 SMP00686 Pentazocine Action Pathway 0.950205179234751 -0.0510773395656286 26 2 0.0119760479041916 167 992 782,476 CACNB1,ATP1A1 SMP00404 Ropivacaine Action Pathway 0.950205179234751 -0.0510773395656286 26 2 0.0119760479041916 167 992 782,476 CACNB1,ATP1A1 SMP00425 Escitalopram Action Pathway 0.950205179234751 -0.0510773395656286 26 2 0.0119760479041916 167 992 782,476 CACNB1,ATP1A1 SMP00679 3-Methylthiofentanyl Action Pathway 0.950205179234751 -0.0510773395656286 26 2 0.0119760479041916 167 992 782,476 CACNB1,ATP1A1 SMP00681 Ethylmorphine Action Pathway 0.950205179234751 -0.0510773395656286 26 2 0.0119760479041916 167 992 782,476 CACNB1,ATP1A1 SMP00684 Buprenorphine Action Pathway 0.950205179234751 -0.0510773395656286 26 2 0.0119760479041916 167 992 782,476 CACNB1,ATP1A1 SMP00672 Propoxyphene Action Pathway 0.950205179234751 -0.0510773395656286 26 2 0.0119760479041916 167 992 782,476 CACNB1,ATP1A1 SMP00690 Ketobemidone Action Pathway 0.950205179234751 -0.0510773395656286 26 2 0.0119760479041916 167 992 782,476 CACNB1,ATP1A1 SMP00392 Benzocaine Action Pathway 0.950205179234751 -0.0510773395656286 26 2 0.0119760479041916 167 992 782,476 CACNB1,ATP1A1 SMP00410 Hydromorphone Action Pathway 0.950205179234751 -0.0510773395656286 26 2 0.0119760479041916 167 992 782,476 CACNB1,ATP1A1 SMP00399 Mepivacaine Action Pathway 0.950205179234751 -0.0510773395656286 26 2 0.0119760479041916 167 992 782,476 CACNB1,ATP1A1 SMP00678 Methadyl Acetate Action Pathway 0.950205179234751 -0.0510773395656286 26 2 0.0119760479041916 167 992 782,476 CACNB1,ATP1A1 SMP00416 Remifentanil Action Pathway 0.950205179234751 -0.0510773395656286 26 2 0.0119760479041916 167 992 782,476 CACNB1,ATP1A1 SMP00671 Tramadol Action Action Pathway 0.950205179234751 -0.0510773395656286 26 2 0.0119760479041916 167 992 782,476 CACNB1,ATP1A1 SMP00393 Bupivacaine Action Pathway 0.950205179234751 -0.0510773395656286 26 2 0.0119760479041916 167 992 782,476 CACNB1,ATP1A1 SMP00396 Dibucaine Action Pathway 0.950205179234751 -0.0510773395656286 26 2 0.0119760479041916 167 992 782,476 CACNB1,ATP1A1 SMP00415 Fentanyl Action Pathway 0.950205179234751 -0.0510773395656286 26 2 0.0119760479041916 167 992 782,476 CACNB1,ATP1A1 SMP00673 Levorphanol Action Pathway 0.950205179234751 -0.0510773395656286 26 2 0.0119760479041916 167 992 782,476 CACNB1,ATP1A1 SMP00401 Prilocaine Action Pathway 0.950205179234751 -0.0510773395656286 26 2 0.0119760479041916 167 992 782,476 CACNB1,ATP1A1 SMP00685 Alvimopan Action Pathway 0.950205179234751 -0.0510773395656286 26 2 0.0119760479041916 167 992 782,476 CACNB1,ATP1A1 SMP00400 Oxybuprocaine Action Pathway 0.950205179234751 -0.0510773395656286 26 2 0.0119760479041916 167 992 782,476 CACNB1,ATP1A1 SMP00394 Chloroprocaine Action Pathway 0.950205179234751 -0.0510773395656286 26 2 0.0119760479041916 167 992 782,476 CACNB1,ATP1A1 SMP00414 Carfentanil Action Pathway 0.950205179234751 -0.0510773395656286 26 2 0.0119760479041916 167 992 782,476 CACNB1,ATP1A1 SMP00397 Levobupivacaine Action Pathway 0.950205179234751 -0.0510773395656286 26 2 0.0119760479041916 167 992 782,476 CACNB1,ATP1A1 SMP00676 Dezocine Action Pathway 0.950205179234751 -0.0510773395656286 26 2 0.0119760479041916 167 992 782,476 CACNB1,ATP1A1 SMP00413 Alfentanil Action Pathway 0.950205179234751 -0.0510773395656286 26 2 0.0119760479041916 167 992 782,476 CACNB1,ATP1A1 SMP00395 Cocaine Action Pathway 0.950205179234751 -0.0510773395656286 26 2 0.0119760479041916 167 992 782,476 CACNB1,ATP1A1 SMP00412 Oxymorphone Action Pathway 0.950205179234751 -0.0510773395656286 26 2 0.0119760479041916 167 992 782,476 CACNB1,ATP1A1 SMP00688 Naloxone Action Pathway 0.950205179234751 -0.0510773395656286 26 2 0.0119760479041916 167 992 782,476 CACNB1,ATP1A1 SMP00403 Proparacaine Action Pathway 0.950205179234751 -0.0510773395656286 26 2 0.0119760479041916 167 992 782,476 CACNB1,ATP1A1 SMP00677 Levomethadyl Acetate Action Action Pathway 0.950205179234751 -0.0510773395656286 26 2 0.0119760479041916 167 992 782,476 CACNB1,ATP1A1 SMP00683 Levallorphan Action Pathway 0.950205179234751 -0.0510773395656286 26 2 0.0119760479041916 167 992 782,476 CACNB1,ATP1A1 SMP00402 Procaine Action Pathway 0.950205179234751 -0.0510773395656286 26 2 0.0119760479041916 167 992 782,476 CACNB1,ATP1A1 SMP00680 Dimethylthiambutene Action Pathway 0.950205179234751 -0.0510773395656286 26 2 0.0119760479041916 167 992 782,476 CACNB1,ATP1A1 SMP00409 Oxycodone Action Pathway 0.950205179234751 -0.0510773395656286 26 2 0.0119760479041916 167 992 782,476 CACNB1,ATP1A1 SMP00691 Nalbuphine Action Pathway 0.957430762037974 -0.0435018717294105 27 2 0.0119760479041916 167 992 782,476 CACNB1,ATP1A1 SMP00423 Desipramine Action Pathway 0.957430762037974 -0.0435018717294105 27 2 0.0119760479041916 167 992 782,476 CACNB1,ATP1A1 SMP00218 Tyrosinemia Type I 0.957653545393315 -0.0432692100596535 17 1 0.00598802395209581 167 992 4282 MIF SMP00498 Dopamine beta-hydroxylase deficiency 0.957653545393315 -0.0432692100596535 17 1 0.00598802395209581 167 992 4282 MIF SMP00533 Monoamine oxidase-a deficiency (MAO-A) 0.957653545393315 -0.0432692100596535 17 1 0.00598802395209581 167 992 4282 MIF SMP00190 Hawkinsinuria 0.957653545393315 -0.0432692100596535 17 1 0.00598802395209581 167 992 4282 MIF SMP00006 Tyrosine Metabolism 0.957653545393315 -0.0432692100596535 17 1 0.00598802395209581 167 992 4282 MIF SMP00169 Alkaptonuria 0.957653545393315 -0.0432692100596535 17 1 0.00598802395209581 167 992 4282 MIF SMP00706 Tenoxicam Action Pathway 0.963651271744066 -0.0370258011222145 28 2 0.0119760479041916 167 992 2053,4048 EPHX2,LTA4H SMP00693 Antrafenine Action Pathway 0.963651271744066 -0.0370258011222145 28 2 0.0119760479041916 167 992 2053,4048 EPHX2,LTA4H SMP00102 Bromfenac Action Pathway 0.963651271744066 -0.0370258011222145 28 2 0.0119760479041916 167 992 4048,2053 LTA4H,EPHX2 SMP00699 Lumiracoxib Action Pathway 0.963651271744066 -0.0370258011222145 28 2 0.0119760479041916 167 992 4048,2053 LTA4H,EPHX2 SMP00098 Ketorolac Action Pathway 0.963651271744066 -0.0370258011222145 28 2 0.0119760479041916 167 992 4048,2053 LTA4H,EPHX2 SMP00106 Meloxicam Action Pathway 0.963651271744066 -0.0370258011222145 28 2 0.0119760479041916 167 992 4048,2053 LTA4H,EPHX2 SMP00707 Salsalate Action Pathway 0.963651271744066 -0.0370258011222145 28 2 0.0119760479041916 167 992 4048,2053 LTA4H,EPHX2 SMP00085 Ketoprofen Action Pathway 0.963651271744066 -0.0370258011222145 28 2 0.0119760479041916 167 992 2053,4048 EPHX2,LTA4H SMP00692 Antipyrine Action Pathway 0.963651271744066 -0.0370258011222145 28 2 0.0119760479041916 167 992 2053,4048 EPHX2,LTA4H SMP00353 Leukotriene C4 Synthesis Deficiency 0.963651271744066 -0.0370258011222145 28 2 0.0119760479041916 167 992 4048,2053 LTA4H,EPHX2 SMP00700 Lornoxicam Action Pathway 0.963651271744066 -0.0370258011222145 28 2 0.0119760479041916 167 992 4048,2053 LTA4H,EPHX2 SMP00701 Phenylbutazone Action Pathway 0.963651271744066 -0.0370258011222145 28 2 0.0119760479041916 167 992 2053,4048 EPHX2,LTA4H SMP00398 Lidocaine (Local Anaesthetic) Action Pathway 0.963651271744066 -0.0370258011222145 28 2 0.0119760479041916 167 992 782,476 CACNB1,ATP1A1 SMP00094 Sulindac Action Pathway 0.963651271744066 -0.0370258011222145 28 2 0.0119760479041916 167 992 4048,2053 LTA4H,EPHX2 SMP00114 Nabumetone Action Pathway 0.963651271744066 -0.0370258011222145 28 2 0.0119760479041916 167 992 2053,4048 EPHX2,LTA4H SMP00109 Mefenamic Acid Action Pathway 0.963651271744066 -0.0370258011222145 28 2 0.0119760479041916 167 992 2053,4048 EPHX2,LTA4H SMP00113 Oxaprozin Action Pathway 0.963651271744066 -0.0370258011222145 28 2 0.0119760479041916 167 992 4048,2053 LTA4H,EPHX2 SMP00702 Nepafenac Action Pathway 0.963651271744066 -0.0370258011222145 28 2 0.0119760479041916 167 992 4048,2053 LTA4H,EPHX2 SMP00698 Magnesium salicylate Action Pathway 0.963651271744066 -0.0370258011222145 28 2 0.0119760479041916 167 992 4048,2053 LTA4H,EPHX2 SMP00289 Diflunisal Action Pathway 0.963651271744066 -0.0370258011222145 28 2 0.0119760479041916 167 992 4048,2053 LTA4H,EPHX2 SMP00708 Salicylate-sodium Action Pathway 0.963651271744066 -0.0370258011222145 28 2 0.0119760479041916 167 992 4048,2053 LTA4H,EPHX2 SMP00077 Piroxicam Action Pathway 0.963651271744066 -0.0370258011222145 28 2 0.0119760479041916 167 992 4048,2053 LTA4H,EPHX2 SMP00083 Acetylsalicylic Acid Action Pathway 0.963651271744066 -0.0370258011222145 28 2 0.0119760479041916 167 992 4048,2053 LTA4H,EPHX2 SMP00710 Acetaminophen Action Pathway 0.963651271744066 -0.0370258011222145 28 2 0.0119760479041916 167 992 4048,2053 LTA4H,EPHX2 SMP00697 Flurbiprofen Action Pathway 0.963651271744066 -0.0370258011222145 28 2 0.0119760479041916 167 992 4048,2053 LTA4H,EPHX2 SMP00084 Etodolac Action Pathway 0.963651271744066 -0.0370258011222145 28 2 0.0119760479041916 167 992 4048,2053 LTA4H,EPHX2 SMP00075 Arachidonic Acid Metabolism 0.963651271744066 -0.0370258011222145 28 2 0.0119760479041916 167 992 2053,4048 EPHX2,LTA4H SMP00696 Fenoprofen Action Pathway 0.963651271744066 -0.0370258011222145 28 2 0.0119760479041916 167 992 4048,2053 LTA4H,EPHX2 SMP00703 Trisalicylate-choline Action Pathway 0.963651271744066 -0.0370258011222145 28 2 0.0119760479041916 167 992 4048,2053 LTA4H,EPHX2 SMP00709 Salicylic Acid Action Pathway 0.963651271744066 -0.0370258011222145 28 2 0.0119760479041916 167 992 4048,2053 LTA4H,EPHX2 SMP00093 Diclofenac Action Pathway 0.963651271744066 -0.0370258011222145 28 2 0.0119760479041916 167 992 4048,2053 LTA4H,EPHX2 SMP00695 Etoricoxib Action Pathway 0.963651271744066 -0.0370258011222145 28 2 0.0119760479041916 167 992 4048,2053 LTA4H,EPHX2 SMP00101 Suprofen Action Pathway 0.963651271744066 -0.0370258011222145 28 2 0.0119760479041916 167 992 4048,2053 LTA4H,EPHX2 SMP00704 Tolmetin Action Pathway 0.963651271744066 -0.0370258011222145 28 2 0.0119760479041916 167 992 4048,2053 LTA4H,EPHX2 SMP00694 Carprofen Action Pathway 0.963651271744066 -0.0370258011222145 28 2 0.0119760479041916 167 992 4048,2053 LTA4H,EPHX2 SMP00705 Tiaprofenic Acid Action Pathway 0.963651271744066 -0.0370258011222145 28 2 0.0119760479041916 167 992 4048,2053 LTA4H,EPHX2 SMP00087 Rofecoxib Action Pathway 0.963651271744066 -0.0370258011222145 28 2 0.0119760479041916 167 992 4048,2053 LTA4H,EPHX2 SMP00116 Valdecoxib Action Pathway 0.963651271744066 -0.0370258011222145 28 2 0.0119760479041916 167 992 4048,2053 LTA4H,EPHX2 SMP00120 Naproxen Action Pathway 0.963651271744066 -0.0370258011222145 28 2 0.0119760479041916 167 992 4048,2053 LTA4H,EPHX2 SMP00405 Codeine Action Pathway 0.968998023055828 -0.0314927072835163 29 2 0.0119760479041916 167 992 782,476 CACNB1,ATP1A1 SMP00104 Indomethacin Action Pathway 0.968998023055828 -0.0314927072835163 29 2 0.0119760479041916 167 992 2053,4048 EPHX2,LTA4H SMP00407 Heroin Action Pathway 0.968998023055828 -0.0314927072835163 29 2 0.0119760479041916 167 992 782,476 CACNB1,ATP1A1 SMP00063 Tryptophan Metabolism 0.970923751069489 -0.0295073399641767 19 1 0.00598802395209581 167 992 847 CAT SMP00422 Imipramine Action Pathway 0.973586901519371 -0.0267681910564992 30 2 0.0119760479041916 167 992 782,476 CACNB1,ATP1A1 SMP00306 Pindolol Action Pathway 0.976223792164939 -0.0240634236022204 57 5 0.029940119760479 167 992 782,476,3784,488,5566 CACNB1,ATP1A1,KCNQ1,ATP2A2,PRKACA SMP00323 Quinidine Action Pathway 0.976223792164939 -0.0240634236022204 57 5 0.029940119760479 167 992 782,476,3784,488,5566 CACNB1,ATP1A1,KCNQ1,ATP2A2,PRKACA SMP00660 Sotalol Action Pathway 0.976223792164939 -0.0240634236022204 57 5 0.029940119760479 167 992 782,3784,476,488,5566 CACNB1,KCNQ1,ATP1A1,ATP2A2,PRKACA SMP00379 Nifedipine Action Pathway 0.976223792164939 -0.0240634236022204 57 5 0.029940119760479 167 992 782,3784,476,488,5566 CACNB1,KCNQ1,ATP1A1,ATP2A2,PRKACA SMP00325 Disopyramide Action Pathway 0.976223792164939 -0.0240634236022204 57 5 0.029940119760479 167 992 782,476,3784,488,5566 CACNB1,ATP1A1,KCNQ1,ATP2A2,PRKACA SMP00669 Practolol Action Pathway 0.976223792164939 -0.0240634236022204 57 5 0.029940119760479 167 992 782,3784,476,488,5566 CACNB1,KCNQ1,ATP1A1,ATP2A2,PRKACA SMP00667 Metipranolol Action Pathway 0.976223792164939 -0.0240634236022204 57 5 0.029940119760479 167 992 782,476,3784,488,5566 CACNB1,ATP1A1,KCNQ1,ATP2A2,PRKACA SMP00380 Nimodipine Action Pathway 0.976223792164939 -0.0240634236022204 57 5 0.029940119760479 167 992 782,476,3784,488,5566 CACNB1,ATP1A1,KCNQ1,ATP2A2,PRKACA SMP00381 Nisoldipine Action Pathway 0.976223792164939 -0.0240634236022204 57 5 0.029940119760479 167 992 782,476,3784,488,5566 CACNB1,ATP1A1,KCNQ1,ATP2A2,PRKACA SMP00659 Timolol Action Pathway 0.976223792164939 -0.0240634236022204 57 5 0.029940119760479 167 992 782,476,3784,488,5566 CACNB1,ATP1A1,KCNQ1,ATP2A2,PRKACA SMP00661 Epinephrine Action Pathway 0.976223792164939 -0.0240634236022204 57 5 0.029940119760479 167 992 782,476,3784,488,5566 CACNB1,ATP1A1,KCNQ1,ATP2A2,PRKACA SMP00324 Procainamide (Antiarrhythmic) Action Pathway 0.976223792164939 -0.0240634236022204 57 5 0.029940119760479 167 992 782,476,3784,488,5566 CACNB1,ATP1A1,KCNQ1,ATP2A2,PRKACA SMP00366 Nebivolol Action Pathway 0.976223792164939 -0.0240634236022204 57 5 0.029940119760479 167 992 782,3784,476,488,5566 CACNB1,KCNQ1,ATP1A1,ATP2A2,PRKACA SMP00377 Felodipine Action Pathway 0.976223792164939 -0.0240634236022204 57 5 0.029940119760479 167 992 782,3784,476,488,5566 CACNB1,KCNQ1,ATP1A1,ATP2A2,PRKACA SMP00296 Acebutolol Action Pathway 0.976223792164939 -0.0240634236022204 57 5 0.029940119760479 167 992 782,476,3784,488,5566 CACNB1,ATP1A1,KCNQ1,ATP2A2,PRKACA SMP00305 Penbutolol Action Pathway 0.976223792164939 -0.0240634236022204 57 5 0.029940119760479 167 992 782,476,3784,488,5566 CACNB1,ATP1A1,KCNQ1,ATP2A2,PRKACA SMP00663 Isoprenaline Action Pathway 0.976223792164939 -0.0240634236022204 57 5 0.029940119760479 167 992 782,3784,476,488,5566 CACNB1,KCNQ1,ATP1A1,ATP2A2,PRKACA SMP00658 Carteolol Action Pathway 0.976223792164939 -0.0240634236022204 57 5 0.029940119760479 167 992 782,476,3784,488,5566 CACNB1,ATP1A1,KCNQ1,ATP2A2,PRKACA SMP00657 Bopindolol Action Pathway 0.976223792164939 -0.0240634236022204 57 5 0.029940119760479 167 992 782,476,3784,488,5566 CACNB1,ATP1A1,KCNQ1,ATP2A2,PRKACA SMP00664 Arbutamine Action Pathway 0.976223792164939 -0.0240634236022204 57 5 0.029940119760479 167 992 782,476,3784,488,5566 CACNB1,ATP1A1,KCNQ1,ATP2A2,PRKACA SMP00588 Muscle/Heart Contraction 0.976223792164939 -0.0240634236022204 57 5 0.029940119760479 167 992 782,476,3784,488,5566 CACNB1,ATP1A1,KCNQ1,ATP2A2,PRKACA SMP00298 Atenolol Action Pathway 0.976223792164939 -0.0240634236022204 57 5 0.029940119760479 167 992 782,476,3784,488,5566 CACNB1,ATP1A1,KCNQ1,ATP2A2,PRKACA SMP00304 Oxprenolol Action Pathway 0.976223792164939 -0.0240634236022204 57 5 0.029940119760479 167 992 782,3784,476,488,5566 CACNB1,KCNQ1,ATP1A1,ATP2A2,PRKACA SMP00332 Ibutilide Action Pathway 0.976223792164939 -0.0240634236022204 57 5 0.029940119760479 167 992 782,476,3784,488,5566 CACNB1,ATP1A1,KCNQ1,ATP2A2,PRKACA SMP00665 Amiodarone Action Pathway 0.976223792164939 -0.0240634236022204 57 5 0.029940119760479 167 992 782,476,3784,488,5566 CACNB1,ATP1A1,KCNQ1,ATP2A2,PRKACA SMP00378 Isradipine Action Pathway 0.976223792164939 -0.0240634236022204 57 5 0.029940119760479 167 992 782,476,3784,488,5566 CACNB1,ATP1A1,KCNQ1,ATP2A2,PRKACA SMP00670 Bupranolol Action Pathway 0.976223792164939 -0.0240634236022204 57 5 0.029940119760479 167 992 782,3784,476,488,5566 CACNB1,KCNQ1,ATP1A1,ATP2A2,PRKACA SMP00303 Nadolol Action Pathway 0.976223792164939 -0.0240634236022204 57 5 0.029940119760479 167 992 782,476,3784,488,5566 CACNB1,ATP1A1,KCNQ1,ATP2A2,PRKACA SMP00297 Alprenolol Action Pathway 0.976223792164939 -0.0240634236022204 57 5 0.029940119760479 167 992 782,476,3784,488,5566 CACNB1,ATP1A1,KCNQ1,ATP2A2,PRKACA SMP00331 Flecainide Action Pathway 0.976223792164939 -0.0240634236022204 57 5 0.029940119760479 167 992 782,476,3784,488,5566 CACNB1,ATP1A1,KCNQ1,ATP2A2,PRKACA SMP00359 Diltiazem Action Pathway 0.976223792164939 -0.0240634236022204 57 5 0.029940119760479 167 992 782,476,3784,488,5566 CACNB1,ATP1A1,KCNQ1,ATP2A2,PRKACA SMP00375 Verapamil Action Pathway 0.976223792164939 -0.0240634236022204 57 5 0.029940119760479 167 992 782,476,3784,488,5566 CACNB1,ATP1A1,KCNQ1,ATP2A2,PRKACA SMP00382 Nitrendipine Action Pathway 0.976223792164939 -0.0240634236022204 57 5 0.029940119760479 167 992 782,476,3784,488,5566 CACNB1,ATP1A1,KCNQ1,ATP2A2,PRKACA SMP00662 Dobutamine Action Pathway 0.976223792164939 -0.0240634236022204 57 5 0.029940119760479 167 992 782,476,3784,488,5566 CACNB1,ATP1A1,KCNQ1,ATP2A2,PRKACA SMP00329 Mexiletine Action Pathway 0.976223792164939 -0.0240634236022204 57 5 0.029940119760479 167 992 782,3784,476,488,5566 CACNB1,KCNQ1,ATP1A1,ATP2A2,PRKACA SMP00302 Metoprolol Action Pathway 0.976223792164939 -0.0240634236022204 57 5 0.029940119760479 167 992 782,476,3784,488,5566 CACNB1,ATP1A1,KCNQ1,ATP2A2,PRKACA SMP00300 Bisoprolol Action Pathway 0.976223792164939 -0.0240634236022204 57 5 0.029940119760479 167 992 782,3784,476,488,5566 CACNB1,KCNQ1,ATP1A1,ATP2A2,PRKACA SMP00376 Amlodipine Action Pathway 0.976223792164939 -0.0240634236022204 57 5 0.029940119760479 167 992 782,476,3784,488,5566 CACNB1,ATP1A1,KCNQ1,ATP2A2,PRKACA SMP00301 Esmolol Action Pathway 0.976223792164939 -0.0240634236022204 57 5 0.029940119760479 167 992 782,476,3784,488,5566 CACNB1,ATP1A1,KCNQ1,ATP2A2,PRKACA SMP00299 Betaxolol Action Pathway 0.976223792164939 -0.0240634236022204 57 5 0.029940119760479 167 992 782,476,3784,488,5566 CACNB1,ATP1A1,KCNQ1,ATP2A2,PRKACA SMP00330 Tocainide Action Pathway 0.976223792164939 -0.0240634236022204 57 5 0.029940119760479 167 992 782,476,3784,488,5566 CACNB1,ATP1A1,KCNQ1,ATP2A2,PRKACA SMP00307 Propranolol Action Pathway 0.976223792164939 -0.0240634236022204 57 5 0.029940119760479 167 992 782,3784,476,488,5566 CACNB1,KCNQ1,ATP1A1,ATP2A2,PRKACA SMP00326 Fosphenytoin (Antiarrhythmic) Action Pathway 0.976223792164939 -0.0240634236022204 57 5 0.029940119760479 167 992 782,476,3784,488,5566 CACNB1,ATP1A1,KCNQ1,ATP2A2,PRKACA SMP00666 Levobunolol Action Pathway 0.976223792164939 -0.0240634236022204 57 5 0.029940119760479 167 992 782,476,3784,488,5566 CACNB1,ATP1A1,KCNQ1,ATP2A2,PRKACA SMP00668 Bevantolol Action Pathway 0.976223792164939 -0.0240634236022204 57 5 0.029940119760479 167 992 782,476,3784,488,5566 CACNB1,ATP1A1,KCNQ1,ATP2A2,PRKACA SMP00426 Fluoxetine Action Pathway 0.977519802945331 -0.0227367285602202 31 2 0.0119760479041916 167 992 782,476 CACNB1,ATP1A1 SMP00368 Labetalol Action Pathway 0.979075538894092 -0.0211464801901554 58 5 0.029940119760479 167 992 782,476,3784,488,5566 CACNB1,ATP1A1,KCNQ1,ATP2A2,PRKACA SMP00367 Carvedilol Action Pathway 0.979075538894092 -0.0211464801901554 58 5 0.029940119760479 167 992 782,3784,476,488,5566 CACNB1,KCNQ1,ATP1A1,ATP2A2,PRKACA SMP00424 Citalopram Action Pathway 0.980886028255024 -0.0192990053148972 32 2 0.0119760479041916 167 992 782,476 CACNB1,ATP1A1 SMP00431 Nicotine Action Pathway 0.980886028255024 -0.0192990053148972 32 2 0.0119760479041916 167 992 782,476 CACNB1,ATP1A1 SMP00408 Methadone Action Pathway 0.980886028255024 -0.0192990053148972 32 2 0.0119760479041916 167 992 782,476 CACNB1,ATP1A1 SMP00328 Lidocaine (Antiarrhythmic) Action Pathway 0.981607258530732 -0.0185639910215651 59 5 0.029940119760479 167 992 782,3784,476,488,5566 CACNB1,KCNQ1,ATP1A1,ATP2A2,PRKACA SMP00096 Celecoxib Action Pathway 0.986220540411779 -0.0138752775730931 34 2 0.0119760479041916 167 992 4048,2053 LTA4H,EPHX2 SMP00078 Chlorothiazide Action Pathway 0.998313240836114 -0.00168818334384907 34 1 0.00598802395209581 167 992 476 ATP1A1 SMP00088 Bumetanide Action Pathway 0.998313240836114 -0.00168818334384907 34 1 0.00598802395209581 167 992 476 ATP1A1 SMP00115 Furosemide Action Pathway 0.998313240836114 -0.00168818334384907 34 1 0.00598802395209581 167 992 476 ATP1A1 SMP00105 Metolazone Action Pathway 0.998313240836114 -0.00168818334384907 34 1 0.00598802395209581 167 992 476 ATP1A1 SMP00197 Lysinuric Protein Intolerance 0.998313240836114 -0.00168818334384907 34 1 0.00598802395209581 167 992 476 ATP1A1 SMP00245 Glucose Transporter Defect (SGLT2) 0.998313240836114 -0.00168818334384907 34 1 0.00598802395209581 167 992 476 ATP1A1 SMP00090 Bendroflumethiazide Action Pathway 0.998313240836114 -0.00168818334384907 34 1 0.00598802395209581 167 992 476 ATP1A1 SMP00100 Hydrochlorothiazide Action Pathway 0.998313240836114 -0.00168818334384907 34 1 0.00598802395209581 167 992 476 ATP1A1 SMP00583 Blue diaper syndrome 0.998313240836114 -0.00168818334384907 34 1 0.00598802395209581 167 992 476 ATP1A1 SMP00135 Eplerenone Action Pathway 0.998313240836114 -0.00168818334384907 34 1 0.00598802395209581 167 992 476 ATP1A1 SMP00483 Kidney Function 0.998313240836114 -0.00168818334384907 34 1 0.00598802395209581 167 992 476 ATP1A1 SMP00081 Methyclothiazide Action Pathway 0.998313240836114 -0.00168818334384907 34 1 0.00598802395209581 167 992 476 ATP1A1 SMP00108 Hydroflumethiazide Action Pathway 0.998313240836114 -0.00168818334384907 34 1 0.00598802395209581 167 992 476 ATP1A1 SMP00723 Cystinuria 0.998313240836114 -0.00168818334384907 34 1 0.00598802395209581 167 992 476 ATP1A1 SMP00134 Spironolactone Action Pathway 0.998313240836114 -0.00168818334384907 34 1 0.00598802395209581 167 992 476 ATP1A1 SMP00118 Torsemide Action Pathway 0.998313240836114 -0.00168818334384907 34 1 0.00598802395209581 167 992 476 ATP1A1 SMP00189 Hartnup Disorder 0.998313240836114 -0.00168818334384907 34 1 0.00598802395209581 167 992 476 ATP1A1 SMP00133 Amiloride Action Pathway 0.998313240836114 -0.00168818334384907 34 1 0.00598802395209581 167 992 476 ATP1A1 SMP00184 Glucose Transporter Defect (SGLT2) 0.998313240836114 -0.00168818334384907 34 1 0.00598802395209581 167 992 476 ATP1A1 SMP00097 Ethacrynic Acid Action Pathway 0.998313240836114 -0.00168818334384907 34 1 0.00598802395209581 167 992 476 ATP1A1 SMP00091 Quinethazone Action Pathway 0.998313240836114 -0.00168818334384907 34 1 0.00598802395209581 167 992 476 ATP1A1 SMP00585 Lysinuric protein intolerance (LPI) 0.998313240836114 -0.00168818334384907 34 1 0.00598802395209581 167 992 476 ATP1A1 SMP00132 Triamterene Action Pathway 0.998313240836114 -0.00168818334384907 34 1 0.00598802395209581 167 992 476 ATP1A1 SMP00103 Cyclothiazide Action Pathway 0.998313240836114 -0.00168818334384907 34 1 0.00598802395209581 167 992 476 ATP1A1 SMP00110 Indapamide Action Pathway 0.998313240836114 -0.00168818334384907 34 1 0.00598802395209581 167 992 476 ATP1A1 SMP00193 Iminoglycinuria 0.998313240836114 -0.00168818334384907 34 1 0.00598802395209581 167 992 476 ATP1A1 SMP00121 Trichlormethiazide Action Pathway 0.998313240836114 -0.00168818334384907 34 1 0.00598802395209581 167 992 476 ATP1A1 SMP00080 Polythiazide Action Pathway 0.998313240836114 -0.00168818334384907 34 1 0.00598802395209581 167 992 476 ATP1A1 SMP00122 Chlorthalidone Action Pathway 0.998313240836114 -0.00168818334384907 34 1 0.00598802395209581 167 992 476 ATP1A1 SMP00455 Homocysteine Degradation 0.999999999995744 -4.25630364286889e-12 2 0 0 167 992 SMP00612 Esomeprazole Metabolism Pathway 0.999999999995744 -4.25630364286889e-12 2 0 0 167 992 SMP00616 Rabeprazole Metabolism Pathway 0.999999999995744 -4.25630364286889e-12 2 0 0 167 992 SMP00613 Omeprazole Metabolism Pathway 0.999999999995744 -4.25630364286889e-12 2 0 0 167 992 SMP00515 Homocystinuria- cystathionine beta-synthase deficiency 0.999999999995744 -4.25630364286889e-12 2 0 0 167 992 SMP00614 Lansoprazole Metabolism Pathway 0.999999999995744 -4.25630364286889e-12 2 0 0 167 992 SMP00615 Pantoprazole Metabolism Pathway 0.999999999995744 -4.25630364286889e-12 2 0 0 167 992 SMP00456 Fatty Acid Biosynthesis 0.999999999995744 -4.25630364286889e-12 2 0 0 167 992 SMP00514 Gamma-cystathionase deficiency (CTH) 0.999999999995744 -4.25630364286889e-12 2 0 0 167 992 SMP00420 Bevacizumab Action Pathway 0.999999999998963 -1.03654324706826e-12 3 0 0 167 992 SMP00653 Rosiglitazone Metabolism Pathway 0.999999999998963 -1.03654324706826e-12 3 0 0 167 992 SMP00126 Phenylacetate Metabolism 0.999999999998963 -1.03654324706826e-12 3 0 0 167 992 SMP00564 Multiple carboxylase deficiency- neonatal or early onset form 0.999999999998963 -1.03654324706826e-12 3 0 0 167 992 SMP00626 Desipramine Metabolism Pathway 0.999999999998963 -1.03654324706826e-12 3 0 0 167 992 SMP00124 Glycerol Phosphate Shuttle 0.999999999998963 -1.03654324706826e-12 3 0 0 167 992 SMP00174 Biotinidase Deficiency 0.999999999998963 -1.03654324706826e-12 3 0 0 167 992 SMP00472 Erlotinib Action Pathway 0.999999999998963 -1.03654324706826e-12 3 0 0 167 992 SMP00066 Biotin Metabolism 0.999999999998963 -1.03654324706826e-12 3 0 0 167 992 SMP00153 Quinapril Action Pathway 1.00000000000043 4.26480357106074e-13 4 0 0 167 992 SMP00623 Heroin Metabolism Pathway 1.00000000000043 4.26480357106074e-13 4 0 0 167 992 SMP00165 Valsartan Action Pathway 1.00000000000043 4.26480357106074e-13 4 0 0 167 992 SMP00618 Fosphenytoin (Antiarrhythmic) Metabolism Pathway 1.00000000000043 4.26480357106074e-13 4 0 0 167 992 SMP00602 Teniposide Metabolism Pathway 1.00000000000043 4.26480357106074e-13 4 0 0 167 992 SMP00150 Lisinopril Action Pathway 1.00000000000043 4.26480357106074e-13 4 0 0 167 992 SMP00633 Felbamate Metabolism Pathway 1.00000000000043 4.26480357106074e-13 4 0 0 167 992 SMP00164 Telmisartan Action Pathway 1.00000000000043 4.26480357106074e-13 4 0 0 167 992 SMP00651 Artemether Metabolism Pathway 1.00000000000043 4.26480357106074e-13 4 0 0 167 992 SMP00170 Aromatic L-Aminoacid Decarboxylase Deficiency 1.00000000000043 4.26480357106074e-13 4 0 0 167 992 SMP00145 Benazepril Action Pathway 1.00000000000043 4.26480357106074e-13 4 0 0 167 992 SMP00620 Lidocaine (Local Anaesthetic) Metabolism Pathway 1.00000000000043 4.26480357106074e-13 4 0 0 167 992 SMP00443 Teniposide Action Pathway 1.00000000000043 4.26480357106074e-13 4 0 0 167 992 SMP00733 Temocapril Action Pathway 1.00000000000043 4.26480357106074e-13 4 0 0 167 992 SMP00621 Codeine Metabolism Pathway 1.00000000000043 4.26480357106074e-13 4 0 0 167 992 SMP00450 Phytanic Acid Peroxisomal Oxidation 1.00000000000043 4.26480357106074e-13 4 0 0 167 992 SMP00152 Perindopril Action Pathway 1.00000000000043 4.26480357106074e-13 4 0 0 167 992 SMP00012 Catecholamine Biosynthesis 1.00000000000043 4.26480357106074e-13 4 0 0 167 992 SMP00149 Fosinopril Action Pathway 1.00000000000043 4.26480357106074e-13 4 0 0 167 992 SMP00065 Ubiquinone Biosynthesis 1.00000000000043 4.26480357106074e-13 4 0 0 167 992 SMP00163 Olmesartan Action Pathway 1.00000000000043 4.26480357106074e-13 4 0 0 167 992 SMP00629 Adefovir Dipivoxil Metabolism Pathway 1.00000000000043 4.26480357106074e-13 4 0 0 167 992 SMP00154 Ramipril Action Pathway 1.00000000000043 4.26480357106074e-13 4 0 0 167 992 SMP00497 Tyrosine hydroxylase deficiency 1.00000000000043 4.26480357106074e-13 4 0 0 167 992 SMP00148 Enalapril Action Pathway 1.00000000000043 4.26480357106074e-13 4 0 0 167 992 SMP00162 Losartan Action Pathway 1.00000000000043 4.26480357106074e-13 4 0 0 167 992 SMP00451 Refsum Disease 1.00000000000043 4.26480357106074e-13 4 0 0 167 992 SMP00155 Rescinnamine Action Pathway 1.00000000000043 4.26480357106074e-13 4 0 0 167 992 SMP00161 Irbesartan Action Pathway 1.00000000000043 4.26480357106074e-13 4 0 0 167 992 SMP00639 Clomipramine Metabolism Pathway 1.00000000000043 4.26480357106074e-13 4 0 0 167 992 SMP00146 Captopril Action Pathway 1.00000000000043 4.26480357106074e-13 4 0 0 167 992 SMP00160 Forasartan Action Pathway 1.00000000000043 4.26480357106074e-13 4 0 0 167 992 SMP00587 Angiotensin Metabolism 1.00000000000043 4.26480357106074e-13 4 0 0 167 992 SMP00159 Eprosartan Action Pathway 1.00000000000043 4.26480357106074e-13 4 0 0 167 992 SMP00147 Cilazapril Action Pathway 1.00000000000043 4.26480357106074e-13 4 0 0 167 992 SMP00630 Tenofovir Metabolism Pathway 1.00000000000043 4.26480357106074e-13 4 0 0 167 992 SMP00156 Spirapril Action Pathway 1.00000000000043 4.26480357106074e-13 4 0 0 167 992 SMP00151 Moexipril Action Pathway 1.00000000000043 4.26480357106074e-13 4 0 0 167 992 SMP00158 Candesartan Action Pathway 1.00000000000043 4.26480357106074e-13 4 0 0 167 992 SMP00157 Trandolapril Action Pathway 1.00000000000043 4.26480357106074e-13 4 0 0 167 992 SMP00631 Prednisone Metabolism Pathway 1.00000000000064 6.40043573696403e-13 1 0 0 167 992 SMP00265 Abciximab Action Pathway 1.00000000000064 6.40043573696403e-13 1 0 0 167 992 SMP00476 Trastuzumab Action Pathway 1.00000000000064 6.40043573696403e-13 1 0 0 167 992 SMP00593 Enalapril Metabolism Pathway 1.00000000000064 6.40043573696403e-13 1 0 0 167 992 SMP00732 Temocapril Metabolism Pathway 1.00000000000064 6.40043573696403e-13 1 0 0 167 992 SMP00632 Prednisolone Metabolism Pathway 1.00000000000064 6.40043573696403e-13 1 0 0 167 992 SMP00473 Gefitinib Action Pathway 1.00000000000064 6.40043573696403e-13 1 0 0 167 992 SMP00261 Ticlopidine Action Pathway 1.00000000000064 6.40043573696403e-13 1 0 0 167 992 SMP00595 Moexipril Metabolism Pathway 1.00000000000064 6.40043573696403e-13 1 0 0 167 992 SMP00475 Panitumumab Action Pathway 1.00000000000064 6.40043573696403e-13 1 0 0 167 992 SMP00647 Thioguanine Metabolism Pathway 1.00000000000064 6.40043573696403e-13 1 0 0 167 992 SMP00474 Cetuximab Action Pathway 1.00000000000064 6.40043573696403e-13 1 0 0 167 992 SMP00591 Benazepril Metabolism Pathway 1.00000000000064 6.40043573696403e-13 1 0 0 167 992 SMP00597 Ramipril Metabolism Pathway 1.00000000000064 6.40043573696403e-13 1 0 0 167 992 SMP00267 Tirofiban Action Pathway 1.00000000000064 6.40043573696403e-13 1 0 0 167 992 SMP00596 Quinapril Metabolism Pathway 1.00000000000064 6.40043573696403e-13 1 0 0 167 992 SMP00617 Cimetidine Metabolism Pathway 1.00000000000064 6.40043573696403e-13 1 0 0 167 992 SMP00421 Vatalanib Action Pathway 1.00000000000064 6.40043573696403e-13 1 0 0 167 992 SMP00592 Cilazapril Metabolism Pathway 1.00000000000064 6.40043573696403e-13 1 0 0 167 992 SMP00036 D-Arginine and D-Ornithine Metabolism 1.00000000000064 6.40043573696403e-13 1 0 0 167 992 SMP00470 Fluorouracil Action Pathway 1.00000000000064 6.40043573696403e-13 1 0 0 167 992 SMP00611 Ticlopidine Metabolism Pathway 1.00000000000064 6.40043573696403e-13 1 0 0 167 992 SMP00599 Trandolapril Metabolism Pathway 1.00000000000064 6.40043573696403e-13 1 0 0 167 992 SMP00263 Cilostazol Action Pathway 1.00000000000064 6.40043573696403e-13 1 0 0 167 992 SMP00594 Fosinopril Metabolism Pathway 1.00000000000064 6.40043573696403e-13 1 0 0 167 992 SMP00598 Spirapril Metabolism Pathway 1.00000000000064 6.40043573696403e-13 1 0 0 167 992 SMP00264 Dipyridamole (Antiplatelet) Action Pathway 1.00000000000064 6.40043573696403e-13 1 0 0 167 992 SMP00440 Prednisone Action Pathway 1.00000000000064 6.40043573696403e-13 1 0 0 167 992 SMP00638 Levomethadyl Acetate Metabolism Pathway 1.00000000000064 6.40043573696403e-13 1 0 0 167 992 SMP00441 Prednisolone Action Pathway 1.00000000000064 6.40043573696403e-13 1 0 0 167 992 SMP00266 Eptifibatide Action Pathway 1.00000000000064 6.40043573696403e-13 1 0 0 167 992 SMP00608 Fluorouracil Metabolism Pathway 1.00000000000064 6.40043573696403e-13 1 0 0 167 992 SMP00055 Alanine Metabolism 1.0000000000025 2.50070165855147e-12 5 0 0 167 992 SMP00352 Primary Hyperoxaluria Type I 1.0000000000025 2.50070165855147e-12 5 0 0 167 992 SMP00350 Pyruvate Carboxylase Deficiency 1.0000000000025 2.50070165855147e-12 5 0 0 167 992 SMP00641 Doxepin Metabolism Pathway 1.0000000000025 2.50070165855147e-12 5 0 0 167 992 SMP00469 Capecitabine Action Pathway 1.0000000000025 2.50070165855147e-12 5 0 0 167 992 SMP00607 Capecitabine Metabolism Pathway 1.0000000000025 2.50070165855147e-12 5 0 0 167 992 SMP00313 Lactic Acidemia 1.0000000000025 2.50070165855147e-12 5 0 0 167 992 SMP00646 Fluoxetine Metabolism Pathway 1.00000000000393 3.93170081385073e-12 6 0 0 167 992 SMP00636 Venlafaxine Metabolism Pathway 1.00000000000393 3.93170081385073e-12 6 0 0 167 992 SMP00628 Nicotine Metabolism Pathway 1.00000000000393 3.93170081385073e-12 6 0 0 167 992 SMP00625 Imipramine Metabolism Pathway 1.00000000000393 3.93170081385073e-12 6 0 0 167 992 SMP00634 Carbamazepine Metabolism Pathway 1.00000000000587 5.8735045813609e-12 7 0 0 167 992 SMP00627 Citalopram Metabolism Pathway 1.00000000000587 5.8735045813609e-12 7 0 0 167 992 SMP00637 Tramadol Metabolism Pathway 1.00000000000587 5.8735045813609e-12 7 0 0 167 992 SMP00041 Sulfate/Sulfite Metabolism 1.00000000000587 5.8735045813609e-12 7 0 0 167 992 SMP00532 Sulfite oxidase deficiency 1.00000000000587 5.8735045813609e-12 7 0 0 167 992 SMP00605 Ifosfamide Metabolism Pathway 1.00000000000702 7.02346892946884e-12 8 0 0 167 992 SMP00028 Caffeine Metabolism 1.00000000000702 7.02346892946884e-12 8 0 0 167 992 SMP00448 Ifosfamide Action Pathway 1.00000000000702 7.02346892946884e-12 8 0 0 167 992 SMP00644 Celecoxib Metabolism Pathway 1.00000000000702 7.02346892946884e-12 8 0 0 167 992 SMP00228 Pantoprazole Action Pathway 1.00000000000839 8.39356176452467e-12 9 0 0 167 992 SMP00232 Cimetidine Action Pathway 1.00000000000839 8.39356176452467e-12 9 0 0 167 992 SMP00351 GABA-Transaminase Deficiency 1.00000000000839 8.39356176452467e-12 9 0 0 167 992 SMP00610 Clopidogrel Metabolism Pathway 1.00000000000839 8.39356176452467e-12 9 0 0 167 992 SMP00225 Esomeprazole Action Pathway 1.00000000000839 8.39356176452467e-12 9 0 0 167 992 SMP00716 Thyroid hormone synthesis 1.00000000000839 8.39356176452467e-12 9 0 0 167 992 SMP00604 Cyclophosphamide Metabolism Pathway 1.00000000000839 8.39356176452467e-12 9 0 0 167 992 SMP00230 Ranitidine Action Pathway 1.00000000000839 8.39356176452467e-12 9 0 0 167 992 SMP00734 Roxatidine acetate Action Pathway 1.00000000000839 8.39356176452467e-12 9 0 0 167 992 SMP00226 Omeprazole Action Pathway 1.00000000000839 8.39356176452467e-12 9 0 0 167 992 SMP00735 Metiamide Action Pathway 1.00000000000839 8.39356176452467e-12 9 0 0 167 992 SMP00260 Clopidogrel Action Pathway 1.00000000000839 8.39356176452467e-12 9 0 0 167 992 SMP00492 Ureidopropionase deficiency 1.00000000000839 8.39356176452467e-12 9 0 0 167 992 SMP00736 Betazole Action Pathway 1.00000000000839 8.39356176452467e-12 9 0 0 167 992 SMP00589 Gastric Acid Production 1.00000000000839 8.39356176452467e-12 9 0 0 167 992 SMP00229 Rabeprazole Action Pathway 1.00000000000839 8.39356176452467e-12 9 0 0 167 992 SMP00233 Nizatidine Action Pathway 1.00000000000839 8.39356176452467e-12 9 0 0 167 992 SMP00493 Carnosinuria- carnosinemia 1.00000000000839 8.39356176452467e-12 9 0 0 167 992 SMP00007 Beta-Alanine Metabolism 1.00000000000839 8.39356176452467e-12 9 0 0 167 992 SMP00227 Lansoprazole Action Pathway 1.00000000000839 8.39356176452467e-12 9 0 0 167 992 SMP00231 Famotidine Action Pathway 1.00000000000839 8.39356176452467e-12 9 0 0 167 992 SMP00246 Pirenzepine Action Pathway 1.00000000000839 8.39356176452467e-12 9 0 0 167 992 SMP00447 Cyclophosphamide Action Pathway 1.00000000000839 8.39356176452467e-12 9 0 0 167 992 SMP00606 Tamoxifen Metabolism Pathway 1.0000000000102 1.020433355551e-11 10 0 0 167 992 SMP00471 Tamoxifen Action Pathway 1.0000000000102 1.020433355551e-11 10 0 0 167 992 SMP00624 Methadone Metabolism Pathway 1.0000000000102 1.020433355551e-11 10 0 0 167 992 SMP00566 17-alpha-hydroxylase deficiency (CYP17) 1.00000000001247 1.24704246995616e-11 11 0 0 167 992 SMP00371 Congenital Lipoid Adrenal Hyperplasia (CLAH) or Lipoid CAH 1.00000000001247 1.24704246995616e-11 11 0 0 167 992 SMP00575 11-beta-hydroxylase deficiency (CYP11B1) 1.00000000001247 1.24704246995616e-11 11 0 0 167 992 SMP00717 Apparent mineralocorticoid excess syndrome 1.00000000001247 1.24704246995616e-11 11 0 0 167 992 SMP00372 Adrenal Hyperplasia Type 5 or Congenital Adrenal Hyperplasia due to 17 Alpha-hydroxylase Deficiency 1.00000000001247 1.24704246995616e-11 11 0 0 167 992 SMP00576 21-hydroxylase deficiency (CYP21) 1.00000000001247 1.24704246995616e-11 11 0 0 167 992 SMP00577 Corticosterone methyl oxidase I deficiency (CMO I) 1.00000000001247 1.24704246995616e-11 11 0 0 167 992 SMP00578 Corticosterone methyl oxidase II deficiency - CMO II 1.00000000001247 1.24704246995616e-11 11 0 0 167 992 SMP00718 3-Beta-Hydroxysteroid Dehydrogenase Deficiency 1.00000000001247 1.24704246995616e-11 11 0 0 167 992 SMP00373 Adrenal Hyperplasia Type 3 or Congenital Adrenal Hyperplasia due to 21-hydroxylase Deficiency 1.00000000001247 1.24704246995616e-11 11 0 0 167 992 SMP00130 Steroidogenesis 1.00000000001247 1.24704246995616e-11 11 0 0 167 992 SMP00068 Androgen and Estrogen Metabolism 1.00000000001318 1.31829843673839e-11 12 0 0 167 992 SMP00565 Aromatase deficiency 1.00000000001318 1.31829843673839e-11 12 0 0 167 992 SMP00356 17-Beta Hydroxysteroid Dehydrogenase III Deficiency 1.00000000001318 1.31829843673839e-11 12 0 0 167 992 SMP00317 Familial Hypercholanemia (FHCA) 1.00000000002169 2.16944959369188e-11 17 0 0 167 992 SMP00316 Zellweger Syndrome 1.00000000002169 2.16944959369188e-11 17 0 0 167 992 SMP00315 Cerebrotendinous Xanthomatosis (CTX) 1.00000000002169 2.16944959369188e-11 17 0 0 167 992 SMP00314 Congenital Bile Acid Synthesis Defect Type II 1.00000000002169 2.16944959369188e-11 17 0 0 167 992 SMP00035 Bile Acid Biosynthesis 1.00000000002169 2.16944959369188e-11 17 0 0 167 992 SMP00318 Congenital Bile Acid Synthesis Defect Type III 1.00000000002169 2.16944959369188e-11 17 0 0 167 992 SMP00720 27-Hydroxylase Deficiency 1.00000000002169 2.16944959369188e-11 17 0 0 167 992 SMP00004 Glycine and Serine Metabolism 1.00000000002984 2.98351908832365e-11 26 0 0 167 992 SMP00484 Dimethylglycine Dehydrogenase Deficiency 1.00000000002984 2.98351908832365e-11 26 0 0 167 992 SMP00244 Sarcosinemia 1.00000000002984 2.98351908832365e-11 26 0 0 167 992 SMP00242 Dimethylglycine Dehydrogenase Deficiency 1.00000000002984 2.98351908832365e-11 26 0 0 167 992 SMP00223 Non Ketotic Hyperglycinemia 1.00000000002984 2.98351908832365e-11 26 0 0 167 992 SMP00179 Dihydropyrimidine Dehydrogenase Deficiency (DHPD) 1.00000000002984 2.98351908832365e-11 26 0 0 167 992 SMP00721 3-Phosphoglycerate dehydrogenase deficiency 1.00000000002984 2.98351908832365e-11 26 0 0 167 992 SMP00485 Hyperglycinemia- non-ketotic 1.00000000002984 2.98351908832365e-11 26 0 0 167 992